ORPHA:254395
Actinic lichen planus
Synonyms: Actinic LP · Lichen planus actinus · Lichen planus subtropicus · Lichen planus tropicus · Lichenoid melanodermatitis · Summertime actinic lichenoid eruption
- Type
- Disease
- Group
- Disorder
- Age of onset
- All ages
- Status
- active
A rare cutaneous lichen planus characterized by the development of photo-distributed lichenoid lesions.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Actinic lichen planus | Actinic LP · Lichen planus actinus · Lichen planus subtropicus · Lichen planus tropicus · Lichenoid melanodermatitis · Summertime actinic lichenoid eruption |
| fr | Lichen plan actinique | Eruption lichénoïde actinique estivale · LP actinique · Lichen plan solaire · Lichen plan subtropical · Lichen plan tropical · Lichen plan tropicalis · Mélanodermatite lichénoïde |
| de | Lichen planus actinicus | Aktinisches lichenoides Sommerexanthem · LP, aktinischer · Lichen planus subtropicus · Lichen planus tropicalis · Melanodermatitis, lichenoide |
| es | Liquen plano actínico | Erupción liquenoide actínica estival · Liquen plano subtropical · Liquen plano tropical · Melanodermatitis liquenoide |
| it | Lichen planus attinico | Eruzione lichenoide actinica estiva · LP attinico · Lichen planus actinus · Lichen planus subtropicale · Lichen planus tropicale · Melanodermatite lichenoide |
| nl | Actinische lichen planus | Actinische LP · Lichen planus actinus · Lichen planus subtropicus · Lichen planus tropicus · Lichenoïde melanodermatitis · Zomerse actinische lichenoïde eruptie |
| pt | Líquen plano actínico | Erupção liquenóide actínica do verão · LP actínico · Líquen plano actínico · Líquen plano subtropical · Líquen plano tropical · Melanodermatite liquenóide |
| pl | Liszaj płaski związany z ekspozycją na UV | Liszaj płaski subtropikalny · Liszaj płaski tropikalny |
| cs | Aktinický lichen planus | Aktinický LP · Lichen planus aktinus · Subtropický lichen planus · Lichen planus tropicus · Lichenoid melanodermatitis · Letní aktinická lichenoidní erupce |
| uk | Актинічний плоский лишай | Actinic LP · Лишай плоский актинічний (Lichen planus actinus) · Лишай субтропічний (Lichen planus subtropicus) · Лишай плаский тропічний (Lichen planus tropicus) · Ліхеноїдний меланодерміт · Літнє виявлення актинічного ліхеноїду |
| zh | 光化性扁平苔藓 | 夏季光化性苔藓样疹 |
| tr | Aktinik liken planus | Aktinik LP · Liken planus aktinus · Liken planus tropikus · Liken planus subtropikus · Likenoid melanodermatit · Yaz dönemi aktinik likenoid erüpsiyonu |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L43.8 | NTBT | attributed | validated |
| ICD-11 | EA91.Y | NTBT | index | validated |
| MONDO | 0016770 | E | validated | |
| UMLS | C0406365 | E | validated | |
| GARD | 12673 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:254370Rare cutaneous lichen planus
rare skin diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/254395
- This record as JSON: /data/d/254395.json