raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:254395

Actinic lichen planus

Synonyms: Actinic LP · Lichen planus actinus · Lichen planus subtropicus · Lichen planus tropicus · Lichenoid melanodermatitis · Summertime actinic lichenoid eruption

Type
Disease
Group
Disorder
Age of onset
All ages
Status
active

A rare cutaneous lichen planus characterized by the development of photo-distributed lichenoid lesions.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enActinic lichen planusActinic LP · Lichen planus actinus · Lichen planus subtropicus · Lichen planus tropicus · Lichenoid melanodermatitis · Summertime actinic lichenoid eruption
frLichen plan actiniqueEruption lichénoïde actinique estivale · LP actinique · Lichen plan solaire · Lichen plan subtropical · Lichen plan tropical · Lichen plan tropicalis · Mélanodermatite lichénoïde
deLichen planus actinicusAktinisches lichenoides Sommerexanthem · LP, aktinischer · Lichen planus subtropicus · Lichen planus tropicalis · Melanodermatitis, lichenoide
esLiquen plano actínicoErupción liquenoide actínica estival · Liquen plano subtropical · Liquen plano tropical · Melanodermatitis liquenoide
itLichen planus attinicoEruzione lichenoide actinica estiva · LP attinico · Lichen planus actinus · Lichen planus subtropicale · Lichen planus tropicale · Melanodermatite lichenoide
nlActinische lichen planusActinische LP · Lichen planus actinus · Lichen planus subtropicus · Lichen planus tropicus · Lichenoïde melanodermatitis · Zomerse actinische lichenoïde eruptie
ptLíquen plano actínicoErupção liquenóide actínica do verão · LP actínico · Líquen plano actínico · Líquen plano subtropical · Líquen plano tropical · Melanodermatite liquenóide
plLiszaj płaski związany z ekspozycją na UVLiszaj płaski subtropikalny · Liszaj płaski tropikalny
csAktinický lichen planusAktinický LP · Lichen planus aktinus · Subtropický lichen planus · Lichen planus tropicus · Lichenoid melanodermatitis · Letní aktinická lichenoidní erupce
ukАктинічний плоский лишайActinic LP · Лишай плоский актинічний (Lichen planus actinus) · Лишай субтропічний (Lichen planus subtropicus) · Лишай плаский тропічний (Lichen planus tropicus) · Ліхеноїдний меланодерміт · Літнє виявлення актинічного ліхеноїду
zh光化性扁平苔藓夏季光化性苔藓样疹
trAktinik liken planusAktinik LP · Liken planus aktinus · Liken planus tropikus · Liken planus subtropikus · Likenoid melanodermatit · Yaz dönemi aktinik likenoid erüpsiyonu

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10L43.8NTBTattributedvalidated
ICD-11EA91.YNTBTindexvalidated
MONDO0016770Evalidated
UMLSC0406365Evalidated
GARD12673Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

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Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card