{"orpha":254395,"name":"Actinic lichen planus","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Actinic LP","Lichen planus actinus","Lichen planus subtropicus","Lichen planus tropicus","Lichenoid melanodermatitis","Summertime actinic lichenoid eruption"],"definition":"A rare cutaneous lichen planus characterized by the development of photo-distributed lichenoid lesions.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-254395/","orphanet_url":"https://www.orpha.net/en/disease/detail/254395","names":{"fr":{"name":"Lichen plan actinique","synonyms":["Eruption lichénoïde actinique estivale","LP actinique","Lichen plan solaire","Lichen plan subtropical","Lichen plan tropical","Lichen plan tropicalis","Mélanodermatite lichénoïde"],"definition":"Le lichen plan (LP) actinique est une variante rare de LP cutané caractérisée par l'appartion de lésions lichéniennes en zones photo-exposées."},"de":{"name":"Lichen planus actinicus","synonyms":["Aktinisches lichenoides Sommerexanthem","LP, aktinischer","Lichen planus subtropicus","Lichen planus tropicalis","Melanodermatitis, lichenoide"],"definition":"Der Aktinische Lichen planus (LP) ist eine seltene Variante des kutanen Lichen planus (s. dort) und gekennzeichnet durch das Auftreten lichenoider Läsionen in lichtexponierten Bereichen der Haut."},"es":{"name":"Liquen plano actínico","synonyms":["Erupción liquenoide actínica estival","Liquen plano subtropical","Liquen plano tropical","Melanodermatitis liquenoide"],"definition":"Es una variante rara del liquen plano cutáneo caracterizado por un desarrollo de lesiones liquenoides distribuidas según la exposición solar."},"it":{"name":"Lichen planus attinico","synonyms":["Eruzione lichenoide actinica estiva","LP attinico","Lichen planus actinus","Lichen planus subtropicale","Lichen planus tropicale","Melanodermatite lichenoide"],"definition":"Il lichen piano (LP) attinico è una variante rara del lichen piano cutaneo (si veda questo termine), caratterizzata dallo sviluppo di lesioni lichenoidi distribuite sulle regioni esposte alla luce."},"nl":{"name":"Actinische lichen planus","synonyms":["Actinische LP","Lichen planus actinus","Lichen planus subtropicus","Lichen planus tropicus","Lichenoïde melanodermatitis","Zomerse actinische lichenoïde eruptie"],"definition":"Een zeldzame, cutane lichen planus, gekarakteriseerd door ontwikkeling van lichenoïde laesies in zones blootgesteld aan licht."},"pt":{"name":"Líquen plano actínico","synonyms":["Erupção liquenóide actínica do verão","LP actínico","Líquen plano actínico","Líquen plano subtropical","Líquen plano tropical","Melanodermatite liquenóide"],"definition":"O líquen plano (LP) actínico é uma variante rara de líquen plano cutâneo (ver este termo), caracterizado pelo desenvolvimento de lesões liquenóides foto-distribuídas."},"pl":{"name":"Liszaj płaski związany z ekspozycją na UV","synonyms":["Liszaj płaski subtropikalny","Liszaj płaski tropikalny"]},"cs":{"name":"Aktinický lichen planus","synonyms":["Aktinický LP","Lichen planus aktinus","Subtropický lichen planus","Lichen planus tropicus","Lichenoid melanodermatitis","Letní aktinická lichenoidní erupce"]},"uk":{"name":"Актинічний плоский лишай","synonyms":["Actinic LP","Лишай плоский актинічний (Lichen planus actinus)","Лишай субтропічний (Lichen planus subtropicus)","Лишай плаский тропічний (Lichen planus tropicus)","Ліхеноїдний меланодерміт","Літнє виявлення актинічного ліхеноїду"],"definition":"A rare cutaneous lichen planus characterized by the development of photo-distributed lichenoid lesions."},"zh":{"name":"光化性扁平苔藓","synonyms":["夏季光化性苔藓样疹"],"definition":"一种罕见的皮肤扁平苔藓，其特征是苔藓样病变的光化性分布。"},"tr":{"name":"Aktinik liken planus","synonyms":["Aktinik LP","Liken planus aktinus","Liken planus tropikus","Liken planus subtropikus","Likenoid melanodermatit","Yaz dönemi aktinik likenoid erüpsiyonu"]}},"xrefs":[{"source":"ICD-10","code":"L43.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EA91.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"365229579"},{"source":"MONDO","code":"0016770","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0406365","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12673","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":254370,"name":"Rare cutaneous lichen planus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}