Linear lichen planus
Synonyms: Blaschkoid LP · Blaschkoid lichen planus · Linear LP
- Type
- Disease
- Group
- Disorder
- Age of onset
- All ages
- Status
- active
Linear lichen planus (LLP), also referred to as Blaschkoid LP, is a rare type of lichen planus characterized by a linear distribution of lichenoid lesions along the lines of Blaschko, which are embryonic pathways of skin development.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Linear lichen planus | Blaschkoid LP · Blaschkoid lichen planus · Linear LP |
| fr | Lichen plan linéaire | LP linéaire · Lichen plan Blaschko-linéaire |
| de | Lichen planus linearis | Blaschkoider Lichen planus · LP, linearer |
| es | Liquen plano lineal | LP blaschkoide · LP linear · Liquen plano blaschkoide |
| it | Lichen planus lineare | LP blaschkoide · LP lineare |
| nl | Lineaire lichen planus | Blaschkoïde LP · Blaschkoïde lichen planus · Lineaire LP |
| pt | Líquen plano linear | LP linear |
| pl | Liszaj płaski linijny | Blaschkoidowy liszaj płaski · LP linii Blaschko · LP linijny |
| cs | Lineární lichen planus | Blaschkoidní LP · Blaschkoidní lichen planus · Lineární LP |
| uk | Лінійний плоский лишай | Червоний плоский лишай · Блашкоїдний LP · Лінійний LP |
| zh | 线型扁平苔藓 | Blaschkoid线扁平苔藓 |
| tr | Lineer liken planus | Doğrusal LP · Blaşkoid LP · Blaşkoid liken planus |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L43.8 | NTBT | attributed | validated |
| ICD-11 | EA91.Y | NTBT | index | validated |
| MONDO | 0016769 | E | validated | |
| UMLS | C0023650 | E | validated | |
| GARD | 11898 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:254370Rare cutaneous lichen planus
rare skin diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/254379
- This record as JSON: /data/d/254379.json