{"orpha":254379,"name":"Linear lichen planus","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Blaschkoid LP","Blaschkoid lichen planus","Linear LP"],"definition":"Linear lichen planus (LLP), also referred to as Blaschkoid LP, is a rare type of lichen planus characterized by a linear distribution of lichenoid lesions along the lines of Blaschko, which are embryonic pathways of skin development.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-254379/","orphanet_url":"https://www.orpha.net/en/disease/detail/254379","names":{"fr":{"name":"Lichen plan linéaire","synonyms":["LP linéaire","Lichen plan Blaschko-linéaire"],"definition":"Le lichen plan (LP) linéaire ou LP blaschkolinéaire est une forme rare de lichen plan caractérisée par une distribution linéaire des lésions lichéniennes le long des lignes de Blaschko."},"de":{"name":"Lichen planus linearis","synonyms":["Blaschkoider Lichen planus","LP, linearer"],"definition":"Der Lineare Lichen planus (LLP), auch Blaschkoider LP genannt, ist ein seltener Typ des Lichen planus und gekennzeichnet durch lineare Verteilung lichenoider Läsionen entlang der Blaschko-Linien, die ein Spiegel der embryonalen Entwicklung der Haut sind."},"es":{"name":"Liquen plano lineal","synonyms":["LP blaschkoide","LP linear","Liquen plano blaschkoide"],"definition":"El liquen plano lineal (LPL), también denominado LP blaschkoide, es una variante poco frecuente de liquen plano caracterizado por una distribución lineal de lesiones liquenoides siguiendo las líneas de Blaschko, que reflejan el patrón de migración celular cutáneo durante el desarrollo embrionario."},"it":{"name":"Lichen planus lineare","synonyms":["LP blaschkoide","LP lineare"],"definition":"Il lichen piano lineare (LLP), noto anche come LP blaschkoide, è una forma rara di LP, caratterizzata dalla distribuzione lineare delle lesioni lichenoidi lungo le linee di Blaschko, che definiscono il pattern dello sviluppo embriologico della cute."},"nl":{"name":"Lineaire lichen planus","synonyms":["Blaschkoïde LP","Blaschkoïde lichen planus","Lineaire LP"],"definition":"Lineaire lichen planus (LLP), ook omschreven als Blaschkoïde LP, is een zeldzaam type van lichen planus, gekenmerkt door een lineaire distributie van lichenoïde laesies langsheen de lijnen van Blaschko, die een weerspiegeling zijn van de embryonale ontwikkeling van de huid."},"pt":{"name":"Líquen plano linear","synonyms":["LP linear"],"definition":"O líquen plano linear (LLP), também conhecido como LP Blaschkóide, é um tipo raro de líquen plano caracterizado por uma distribuição linear de lesões liquenóides ao longo das linhas de Blaschko, que são vias embriónicas de desenvolvimento de pele."},"pl":{"name":"Liszaj płaski linijny","synonyms":["Blaschkoidowy liszaj płaski","LP linii Blaschko","LP linijny"]},"cs":{"name":"Lineární lichen planus","synonyms":["Blaschkoidní LP","Blaschkoidní lichen planus","Lineární LP"]},"uk":{"name":"Лінійний плоский лишай","synonyms":["Червоний плоский лишай","Блашкоїдний LP","Лінійний LP"],"definition":"Linear lichen planus (LLP), also referred to as Blaschkoid LP, is a rare type of lichen planus characterized by a linear distribution of lichenoid lesions along the lines of Blaschko, which are embryonic pathways of skin development."},"zh":{"name":"线型扁平苔藓","synonyms":["Blaschkoid线扁平苔藓"],"definition":"线性扁平苔藓(LLP)，又称Blaschkoid LP，是一种罕见的扁平苔藓，其特征是沿皮肤发育的胚胎途径即Blaschko线呈线性分布。"},"tr":{"name":"Lineer liken planus","synonyms":["Doğrusal LP","Blaşkoid LP","Blaşkoid liken planus"]}},"xrefs":[{"source":"ICD-10","code":"L43.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EA91.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"7180779"},{"source":"MONDO","code":"0016769","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0023650","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"11898","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":254370,"name":"Rare cutaneous lichen planus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}