ORPHA:252006
Yolk sac tumor of central nervous system
Synonyms: Endodermal sinus tumor of CNS · Endodermal sinus tumor of central nervous system · Intracranial endodermal sinus tumor · Intracranial yolk sac tumor · Yolk sac tumor of CNS
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Status
- active
Orphadata ships no English definition for this code.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Yolk sac tumor of central nervous system | Endodermal sinus tumor of CNS · Endodermal sinus tumor of central nervous system · Intracranial endodermal sinus tumor · Intracranial yolk sac tumor · Yolk sac tumor of CNS |
| fr | Tumeur du sac vitellin du système nerveux central | Tumeur du sac vitellin du SNC · Tumeur du sinus endodermique du système nerveux central · Tumeur intracrânienne du sac vitellin · Tumeur intracrânienne du sinus endodermique |
| de | Dottersacktumor des Zentralnervensystems | Dottersacktumor, intrakranieller · Endodermaler Sinustumor des ZNS |
| es | Tumor del saco vitelino del sistema nervioso central | Tumor intracraneal del seno endodérmico · Tumor del saco vitelino del SNC · Tumor del seno endodérmico del SNC · Tumor del seno endodérmico del sistema nervioso central · Tumor intracraneal del saco vitelino |
| it | Tumore del sacco vitellino del sistema nervoso centrale | Tumore del sacco vitellino del SNC · Tumore del seno endodermico del SNC · Tumore del seno endodermico del sistema nervoso centrale · Tumore intracranico del sacco vitellino · Tumore intracranico del seno endodermico |
| nl | Dooierzaktumor van centraal zenuwstelsel | Dooierzaktumor van CZS · Intracraniële dooierzaktumor · Intracraniële tumor van endodermale sinus · Tumor van endodermale sinus van CZS · Tumor van endodermale sinus van centraal zenuwstelsel |
| pt | Tumor do saco vitelino do sistema nervoso central | Tumor do saco vitelino intracraniano · Tumor do seio endodérmico do sistema nervoso central · Tumor do seio endodérmico intracraniano |
| pl | Guz pęcherzyka żółtkowego centralnego układu nerwowego | Guz pęcherzyka żółtkowego CUN · Wewnątrzczaszkowy guz zawierający utkanie guza pęcherzyka żółtkowego |
| cs | Nádor centrálního nervového systému ze žloutkového váčku | Nádor endodermálního sinu CNS · Nádor endodermálního sinu centrálního nervového systému · Intrakraniální endodermální sinusový nádor · Nádor CNS ze žloutkového vácku · Intrakraniální nádor ze žloutkového váčku · Nádor CNS ze žloutkového váčku |
| uk | Пухлина жовткового мішка центральної нервової системи | Ендодермальна синусова пухлина центральної нервової системи · Ендодермальна синусова пухлина ЦНС · Внутрішньочерепна ендодермальна пухлина пазухи · Внутрішньочерепна пухлина жовткового мішка · Пухлина жовткового мішка ЦНС |
| zh | 中枢神经系统卵黄囊瘤 | 中枢神经系统内胚层窦瘤 |
| tr | Merkezi sinir sisteminin yolk kesesi tümörü | CNS'nin yolk kesesi tümörü · İntrakraniyal yolk kesesi tümörü · CNS'nin endodermal sinüs tümörü · İntrakraniyal endodermal sinüs tümörü · Merkezi sinir sisteminin endodermal sinüs tümörü |
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C72.9 | NTBT | attributed | validated |
| ICD-11 | 2A00.1Y | NTBT | index | validated |
| MONDO | 0016739 | E | validated | |
| UMLS | C1337040 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:251995Primary germ cell tumor of central nervous system
rare neurological diseases; rare neoplastic diseases; rare transplant-related disorders - ORPHA:876Yolk sac tumor
rare neoplastic diseases; rare transplant-related disorders
No children.
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Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/252006
- This record as JSON: /data/d/252006.json