{"orpha":252006,"name":"Yolk sac tumor of central nervous system","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Endodermal sinus tumor of CNS","Endodermal sinus tumor of central nervous system","Intracranial endodermal sinus tumor","Intracranial yolk sac tumor","Yolk sac tumor of CNS"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-252006/","orphanet_url":"https://www.orpha.net/en/disease/detail/252006","names":{"fr":{"name":"Tumeur du sac vitellin du système nerveux central","synonyms":["Tumeur du sac vitellin du SNC","Tumeur du sinus endodermique du système nerveux central","Tumeur intracrânienne du sac vitellin","Tumeur intracrânienne du sinus endodermique"]},"de":{"name":"Dottersacktumor des Zentralnervensystems","synonyms":["Dottersacktumor, intrakranieller","Endodermaler Sinustumor des ZNS"]},"es":{"name":"Tumor del saco vitelino del sistema nervioso central","synonyms":["Tumor intracraneal del seno endodérmico","Tumor del saco vitelino del SNC","Tumor del seno endodérmico del SNC","Tumor del seno endodérmico del sistema nervioso central","Tumor intracraneal del saco vitelino"]},"it":{"name":"Tumore del sacco vitellino del sistema nervoso centrale","synonyms":["Tumore del sacco vitellino del SNC","Tumore del seno endodermico del SNC","Tumore del seno endodermico del sistema nervoso centrale","Tumore intracranico del sacco vitellino","Tumore intracranico del seno endodermico"]},"nl":{"name":"Dooierzaktumor van centraal zenuwstelsel","synonyms":["Dooierzaktumor van CZS","Intracraniële dooierzaktumor","Intracraniële tumor van endodermale sinus","Tumor van endodermale sinus van CZS","Tumor van endodermale sinus van centraal zenuwstelsel"]},"pt":{"name":"Tumor do saco vitelino do sistema nervoso central","synonyms":["Tumor do saco vitelino intracraniano","Tumor do seio endodérmico do sistema nervoso central","Tumor do seio endodérmico intracraniano"]},"pl":{"name":"Guz pęcherzyka żółtkowego centralnego układu nerwowego","synonyms":["Guz pęcherzyka żółtkowego CUN","Wewnątrzczaszkowy guz zawierający utkanie guza pęcherzyka żółtkowego"]},"cs":{"name":"Nádor centrálního nervového systému ze žloutkového váčku","synonyms":["Nádor endodermálního sinu CNS","Nádor endodermálního sinu centrálního nervového systému","Intrakraniální endodermální sinusový nádor","Nádor CNS ze žloutkového vácku","Intrakraniální nádor ze žloutkového váčku","Nádor CNS ze žloutkového váčku"]},"uk":{"name":"Пухлина жовткового мішка центральної нервової системи","synonyms":["Ендодермальна синусова пухлина центральної нервової системи","Ендодермальна синусова пухлина ЦНС","Внутрішньочерепна ендодермальна пухлина пазухи","Внутрішньочерепна пухлина жовткового мішка","Пухлина жовткового мішка ЦНС"]},"zh":{"name":"中枢神经系统卵黄囊瘤","synonyms":["中枢神经系统内胚层窦瘤"]},"tr":{"name":"Merkezi sinir sisteminin yolk kesesi tümörü","synonyms":["CNS'nin yolk kesesi tümörü","İntrakraniyal yolk kesesi tümörü","CNS'nin endodermal sinüs tümörü","İntrakraniyal endodermal sinüs tümörü","Merkezi sinir sisteminin endodermal sinüs tümörü"]}},"xrefs":[{"source":"ICD-10","code":"C72.9","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2A00.1Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1023155823"},{"source":"MONDO","code":"0016739","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1337040","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":251995,"name":"Primary germ cell tumor of central nervous system","classifications":[181,202,233]},{"orpha":876,"name":"Yolk sac tumor","classifications":[202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}