ORPHA:251902
Atypical papilloma of choroid plexus
Synonyms: Atypical CPP · Atypical choroid plexus papilloma
- Type
- Disease
- Group
- Disorder
- Status
- active
A very rare type of choroid plexus tumor that, contrary to papilloma of the choroid plexus, has an increased likelihood of progression to carcinoma and of recurrence. It displays brisk mitoses, nuclear pleomorphism, raised cellular density, obscurity of the papillary growth pattern, and cell necrosis.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Atypical papilloma of choroid plexus | Atypical CPP · Atypical choroid plexus papilloma |
| fr | Papillome atypique des plexus choroïdes | CPP atypique |
| de | Choroidplexuspapillom, atypisches | CPP, atypisches |
| es | Papiloma atípico del plexo coroideo | PPC atípico · Papiloma del plexo coroideo atípico |
| it | Papilloma atipico del plesso corioideo | |
| nl | Atypisch papilloom van plexus choroideus | Atypisch plexus choroideus-papilloom · Atypisch CPP |
| pt | Papiloma atípico do plexo coróide | |
| pl | Atypowy brodawczak splotu naczyniówkowego | = en |
| cs | Atypický papilom choroidálního plexu | = en |
| uk | Атипова папілома судинного сплетіння | Атипова папілома судинного сплетіння · Атиповий CPP |
| zh | 非典型乳头状脉络丛瘤 | 非典型乳头状脉络丛瘤 |
| tr | Koroid pleksusun atipik papilloması | Atipik CPP · Atipik koroid pleksus papillom |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D33.1 | NTBT | attributed | validated |
| ICD-11 | 2A00.22 | NTBT | index | validated |
| MONDO | 0002684 | E | validated | |
| UMLS | C1266176 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:251896Choroid plexus tumor
rare neurological diseases; rare neoplastic diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/251902
- This record as JSON: /data/d/251902.json