ORPHA:251332
Unexplained long-lasting fever/inflammatory syndrome
Synonyms: Persistent fever/inflammation of unknown origin
- Type
- Disease
- Group
- Disorder
- Age of onset
- All ages
- Status
- active
A rare systemic disease characterized by febrile illness (body temperature >38.3°C on several occasions) or inflammation (elevated serum C-reactive protein and erythrocyte sedimentation rate) lasting at least three weeks and for which no specific diagnosis is achieved despite extended diagnostics.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Unexplained long-lasting fever/inflammatory syndrome | Persistent fever/inflammation of unknown origin |
| fr | Syndrome inflammatoire/fièvre de longue durée inexpliquée | Fièvre/inflammation prolongée d'origine indéterminée |
| de | Fieber-Syndrom, langanhaltendes unerklärbares | Persistierendes Fieber/Anhaltende Inflammation unbekannter Ursache |
| es | Fiebre inexplicada de larga duración/síndrome inflamatorio | Fiebre persistente/inflamación de origen desconocido |
| it | Sindrome infiammatoria/febbre di lunga durata ad eziologia non nota | |
| nl | Onverklaarbare langdurige koorts/inflammatoir syndroom | Persisterende koorts/inflammatie van ongekende oorsprong |
| pt | Síndrome inflamatório/febre de longa duração, não explicado | |
| pl | Niewyjaśniona długotrwała gorączka/zespół zapalny | = en |
| cs | Syndrom nevysvětlitelné dlouhotrvající horečky či zánětu | = en |
| uk | Незрозуміла тривала лихоманка/запальний синдром | Стійка лихоманка/запалення невідомого походження |
| zh | 原因不明的长期发热/炎症综合征 | 原因不明的持续发热/炎症综合征 |
| tr | Açıklanamayan uzun süreli ateş / inflamatuar sendrom | Kalıcı ateş / kaynağı bilinmeyen inflamasyon |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | R50.8 | NTBT | attributed | validated |
| ICD-11 | MG26 | NTBT | attributed | validated |
| MONDO | 0016666 | E | validated | |
| UMLS | C5679630 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (2):
- ORPHA:280373Rare pediatric systemic disease
rare systemic or rheumatologic diseases of childhood - ORPHA:182222Rare systemic disease
rare systemic and rheumatological diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/251332
- This record as JSON: /data/d/251332.json