raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:251325

Drug-induced vasculitis

Type
Disease
Group
Disorder
Status
active

A rare secondary vasculitis characterized by inflammation of blood vessels caused by various drugs, including antibiotics, anti-tumor necrosis factor-alpha agents, immunotherapeutic drugs, and psychoactive agents, among others. The skin is most commonly affected, but other tissues and organs, such as the subcutis, kidneys, or lungs, may also be involved. Systemic disease develops only in a minority of patients, typically when treated with the causative drug over a prolonged period of time. Presenting signs and symptoms include skin rash, myalgia, arthralgia, fever, and malaise.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enDrug-induced vasculitis
frVascularite induite par les médicaments
deVaskulitis, Medikamenten-induzierte
esVasculitis inducida por fármacosVasculitis inducida por medicamentos
itVasculite indotta da farmaci
nlMedicatiegeïnduceerde vasculitis
ptVasculite induzida por fármacos
plZapalenie naczyń indukowane lekami
csLéky indukovaná vaskulitida
ukМедикаментозний васкуліт
zh药物性血管炎
trİlaca bağlı vaskülit

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10M31.8NTBTattributedvalidated
ICD-114A85.03Especificvalidated
MONDO0016664Evalidated
UMLSC0340672Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

  • ORPHA:445197Secondary vasculitis
    rare systemic and rheumatological diseases; rare circulatory system diseases; rare systemic or rheumatologic diseases of childhood

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card