ORPHA:250831
Logopenic progressive aphasia
Synonyms: LPA · Logopenic primary progressive aphasia · Logopenic variant PPA
- Type
- Disease
- Group
- Disorder
- Inheritance
- Multigenic/multifactorial, Not applicable
- Age of onset
- Adult
- Status
- active
Logopenic progressive aphasia (lv-PPA) is a form of primary progressive aphasia (PPA), characterized by impaired single-word retrieval and naming and impaired repetition with spared single-word comprehension and object knowledge.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Logopenic progressive aphasia | LPA · Logopenic primary progressive aphasia · Logopenic variant PPA |
| fr | Aphasie primaire progressive logopénique | APP logopénique |
| de | Aphasie, logopenische progressive | LPA · Logopenische Aphasie, primäre progrediente · PPA (Primäre progrediente Aphasie), logopenische Variante |
| es | Afasia logopénica progresiva | Afasia primaria logopénica progresiva · Variante logopénica de la APP |
| it | Afasia progressiva logopenica | Afasia primitiva progressiva logopenica · LPA · PPA, variante logopenica |
| nl | Logopenische progressieve afasie | LPA · Logopenische primaire progressieve afasie · Logopenische variante PPA |
| pt | Afasia progressiva logopenica | Afasia progressiva primária logopenica · LPA · variante logopenica de APP |
| pl | Postępująca afazja logopeniczna | Logopeniczny wariant PPA · LPA · Pierwotna postępująca afazja logopeniczna |
| cs | Logopenická progresivní afázie | LPA · Logopenická primární progresivní afázie · Logopenická varianta PPA |
| uk | Логопенічна прогресуюча афазія | Логопенічна первинна прогресуюча афазія · Логопенічний варіант PPA · LPA |
| zh | 非流利性进行性失语 | Logopenic型原发性进行性失语 |
| tr | Logopenik ilerleyici afazi | LPA · Logopenik varyant PPA · Logopenik primer ilerleyici afazi |
Definition in:
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G31.0 | NTBT | attributed | validated |
| ICD-11 | 6D83 | NTBT | index | validated |
| MONDO | 0016644 | E | validated | |
| UMLS | C4274665 | E | validated | |
| GARD | 10791 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:95432Primary progressive aphasia
rare neurological diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/250831
- This record as JSON: /data/d/250831.json