{"orpha":250831,"name":"Logopenic progressive aphasia","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["LPA","Logopenic primary progressive aphasia","Logopenic variant PPA"],"definition":"Logopenic progressive aphasia (lv-PPA) is a form of primary progressive aphasia (PPA), characterized by impaired single-word retrieval and naming and impaired repetition with spared single-word comprehension and object knowledge.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-250831/","orphanet_url":"https://www.orpha.net/en/disease/detail/250831","names":{"fr":{"name":"Aphasie primaire progressive logopénique","synonyms":["APP logopénique"],"definition":"L'aphasie primaire progressive logopénique (APP logopénique) est une forme d'aphasie primaire progressive (APP) caractérisée par une difficulté à trouver et à nommer certains mots, des difficultés de répétition, avec une compréhension et une connaissance intactes."},"de":{"name":"Aphasie, logopenische progressive","synonyms":["LPA","Logopenische Aphasie, primäre progrediente","PPA (Primäre progrediente Aphasie), logopenische Variante"]},"es":{"name":"Afasia logopénica progresiva","synonyms":["Afasia primaria logopénica progresiva","Variante logopénica de la APP"],"definition":"Es una forma de afasia progresiva primaria (APP) caracterizada por una afectación de la recuperación y denominación de palabras sueltas y una alteración de la repetición con poca comprensión de palabras sueltas y conocimiento de objetos."},"it":{"name":"Afasia progressiva logopenica","synonyms":["Afasia primitiva progressiva logopenica","LPA","PPA, variante logopenica"]},"nl":{"name":"Logopenische progressieve afasie","synonyms":["LPA","Logopenische primaire progressieve afasie","Logopenische variante PPA"],"definition":"'Logopenische progressieve afasie (lv-PPA) is een vorm van primaire progressieve afasie (PPA; zie deze term) die wordt gekarakteriseerd door moeite bij het vinden en benoemen van een woord alsook moeilijkheden bij het herhalen, met het behoud van begrip en kennis. '"},"pt":{"name":"Afasia progressiva logopenica","synonyms":["Afasia progressiva primária logopenica","LPA","variante logopenica de APP"]},"pl":{"name":"Postępująca afazja logopeniczna","synonyms":["Logopeniczny wariant PPA","LPA","Pierwotna postępująca afazja logopeniczna"]},"cs":{"name":"Logopenická progresivní afázie","synonyms":["LPA","Logopenická primární progresivní afázie","Logopenická varianta PPA"]},"uk":{"name":"Логопенічна прогресуюча афазія","synonyms":["Логопенічна первинна прогресуюча афазія","Логопенічний варіант PPA","LPA"],"definition":"Logopenic progressive aphasia (lv-PPA) is a form of primary progressive aphasia (PPA; see this term), characterized by impaired single-word retrieval and naming and impaired repetition with spared single-word comprehension and object knowledge."},"zh":{"name":"非流利性进行性失语","synonyms":["Logopenic型原发性进行性失语"],"definition":"进行性失语症Logopenic型（lv-PPA）是原发性进行性失语（PPA）的一种类型，其特征是单个词语检索和命名能力受损，单个词语理解与客观知识复述能力受损。"},"tr":{"name":"Logopenik ilerleyici afazi","synonyms":["LPA","Logopenik varyant PPA","Logopenik primer ilerleyici afazi"]}},"xrefs":[{"source":"ICD-10","code":"G31.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"6D83","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"456482023"},{"source":"MONDO","code":"0016644","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4274665","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"10791","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":95432,"name":"Primary progressive aphasia","classifications":[181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Multigenic/multifactorial","Not applicable"],"onset":["Adult"],"prevalence":[],"phenotypes":null}