Ileal pouch anal anastomosis related faecal incontinence
- Type
- Particular clinical situation in a disease or syndrome
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
A rare intestinal disorder characterized by the inability to control the passage of rectal contents (feces, gas) through the anus following ileal pouch-anal anastomosis surgery. Fecal incontinence is usually more frequent during the night than during daytime. The condition generally worsens over time, with a significant negative impact on the quality of life of the patient.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Ileal pouch anal anastomosis related faecal incontinence | |
| fr | Incontinence fécale liée à une anastomose iléo-anale avec poche | |
| de | Stuhlinkontinenz bei Ileum-pouch-anale Anastomose | |
| es | Tratamiento de la incontinencia fecal ligada a una anastomosis íleo-anal con bolsa | |
| it | Anastomosi ileoanale con reservoir associata a incontinenza fecale | |
| nl | Fecale incontinentie gerelateerd aan ileoanale anastomose met pouch | |
| pt | Incontinência fecal relacionada com anastomose anal da bolsa ilíaca | |
| pl | Wewnętrzny zbiornik jelitowy związany z nietrzymaniem kału | |
| cs | Fekální inkontinence v důsledku ileo pouch anální anastomózy | |
| uk | Нетримання калу, повязане з анальним анастомозом | |
| zh | 回肠储袋肛管吻合术相关大便失禁 | |
| tr | İleal kese anal anastomozla -ilişkili fekal inkontinans |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | K91.8 | NTBT | attributed | validated |
| ICD-11 | DE2Y | NTBT | attributed | validated |
| UMLS | C5680932 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:117569Rare intestinal disease
rare gastroenterological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | 1-9 / 100 000 | 3 / 100 000 | Europe | Value and class | Validated | European Medicines Agency 2009[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/238621
- This record as JSON: /data/d/238621.json