raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:231416

Regional variant of Guillain-Barré syndrome

Synonyms: Regional variant of GBS

Type
Clinical group
Group
Group of disorders
Inheritance
Multigenic/multifactorial, Not applicable
Age of onset
All ages
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRegional variant of Guillain-Barré syndromeRegional variant of GBS
frVariant régional du syndrome de Guillain-BarréVariant régional du SGB
deRegionale Variante des Guillain-Barré-Syndroms
esVariante regional del síndrome de Guillain-BarréVariante regional del GBS
itVariante regionale della sindrome di Guillain-BarréVariante regionale di GBS
nlRegionale variant van syndroom van Guillain-BarréRegionale variant van GBS
ptVariante regional do síndrome de Guillain-Barré
plRegionalny wariant zespołu Guillaina i BarrégoRegionalny wariant GBS
csRegionální varianta Guillainova-Barrého syndromuRegionální varianta GBS · Regionální varianta Guillain-Barrého syndromu
ukРегіональний варіант синдрому Гійєна-БарреРегіональний варіант GBS
zh吉兰-巴雷综合征局部变体GBS局部变体
trGuillain-Barrè sendromunun bölgesel varyantıGBS'nin bölgesel varyantı
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO16494Evalidated
UMLSC5679835Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (4):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card