White fibrous papulosis of the neck
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
White fibrous papulosis of the neck is a rare, acquired, dermal elastic tissue disorder characterized by multiple, 2-3 mm sized, non-confluent, asymptomatic, white or pale-colored, non-follicular, firm papular lesions occurring predominantly on the lateral or posterior aspects of the neck. Other, rarely reported sites include inferior axillae, central mid-back and upper sternal region.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | White fibrous papulosis of the neck | |
| fr | Papulose fibreuse blanche du cou | |
| de | Papulose der Halsregion, fibröse weiße | |
| es | Papulosis fibrosa blanca del cuello | |
| it | Papulosi fibrosa bianca del collo | |
| nl | Witte vezelige papulose van hals | |
| pt | Papulose de fibras brancas, do pescoço | |
| pl | Białe włókniste grudki na szyi | |
| cs | Bílá fibrózní papulóza krku | |
| uk | Білий фіброзний папулез шиї | |
| zh | 颈部白色纤维性丘疹 | |
| tr | Boynun beyaz fibröz papülozu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | L98.8 | NTBT | attributed | validated |
| ICD-11 | EE41.Y | NTBT | index | validated |
| MONDO | 0016447 | E | validated | |
| UMLS | C4706484 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/228290
- This record as JSON: /data/d/228290.json