{"orpha":228290,"name":"White fibrous papulosis of the neck","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"White fibrous papulosis of the neck is a rare, acquired, dermal elastic tissue disorder characterized by multiple, 2-3 mm sized, non-confluent, asymptomatic, white or pale-colored, non-follicular, firm papular lesions occurring predominantly on the lateral or posterior aspects of the neck. Other, rarely reported sites include inferior axillae, central mid-back and upper sternal region.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-228290/","orphanet_url":"https://www.orpha.net/en/disease/detail/228290","names":{"fr":{"name":"Papulose fibreuse blanche du cou","definition":"La papulose fibreuse blanche du cou est un trouble rare et acquis du tissu dermique élastique. Elle se caractérise par la présence de multiples lésions papuleuses fermes, non folliculaires, non confluentes, asymptomatiques, de coloration blanche ou pâle, et de 2 à 3 mm de taille. Elles sont surtout localisées sur la partie latérale ou postérieure du cou. Dans de rares cas, les autres sites rapportés incluent la partie inférieure de l'aisselle, la partie centrale du milieu du dos et la région supérieure du sternum."},"de":{"name":"Papulose der Halsregion, fibröse weiße","definition":"Die weiße fibröse Papulose des Halses ist eine seltene, erworbene Erkrankung des elastischen Hautgewebes, die durch multiple, 2-3 mm große, nicht konfluierende, asymptomatische, weiße oder blass gefärbte, nicht-follikuläre, feste papulöse Läsionen gekennzeichnet ist, die vorwiegend an den lateralen oder posterioren Aspekten des Halses auftreten. Andere, selten berichtete Stellen sind die unteren Axillen, der zentrale mittlere Rücken und die obere Sternumregion."},"es":{"name":"Papulosis fibrosa blanca del cuello","definition":"La papulosis fibrosa blanca del cuello es un proceso adquirido poco frecuente del tejido dérmico elástico. Se caracteriza por múltiples pápulas, duras al tacto, no foliculares, de 2-3 mm de tamaño, de color blanco o pálido, no confluentes, asintomáticas, de consistencia dura, localizadas preferentemente en la región lateral o posterior del cuello. Otras regiones raramente descritas incluyen la zona inferior de las axilas, la zona central de la espalda y la parte superior del esternón."},"it":{"name":"Papulosi fibrosa bianca del collo","definition":"La papulosi fibrosa bianca del collo è una malattia rara e acquisita del tessuto elastico del derma. È caratterizzata da lesioni papulari multiple, delle dimensioni di 2-3 mm, non confluenti, asintomatiche, di colore bianco o chiaro, non follicolari e solide, che si localizzano soprattutto nell'area laterale o posteriore del collo. Raramente si localizzano nella porzione inferiore delle ascelle, al centro della schiena e nella parte superiore dello sterno."},"nl":{"name":"Witte vezelige papulose van hals","definition":"Witte fibreuze papulose van de hals is een zeldzame, verworven stoornis van het elastisch huidweefsel en wordt gekarakteriseerd door meerdere, niet samenvloeiende, asymptomatische, witte of licht gekleurde, niet-folliculaire, stevige papulaire letsels met een omvang van 2-3 mm die voornamelijk voorkomen op de zijkanten of achterzijde van de nek. Andere, zelden gerapporteerde plaatsen zijn de onderste zones van de oksels, de centrale middenrug en de bovenste zones van de borst."},"pt":{"name":"Papulose de fibras brancas, do pescoço"},"pl":{"name":"Białe włókniste grudki na szyi"},"cs":{"name":"Bílá fibrózní papulóza krku"},"uk":{"name":"Білий фіброзний папулез шиї","definition":"White fibrous papulosis of the neck is a rare, acquired, dermal elastic tissue disorder characterized by multiple, 2-3 mm sized, non-confluent, asymptomatic, white or pale-colored, non-follicular, firm papular lesions occurring predominantly on the lateral or posterior aspects of the neck. Other, rarely reported sites include inferior axillae, central mid-back and upper sternal region."},"zh":{"name":"颈部白色纤维性丘疹","definition":"颈部白色纤维性丘疹病是一种罕见的获得性皮肤弹性组织疾病，其特征是多发的，2-3毫米大小，非汇合性，无症状，白色或浅色，非滤泡性，坚实的丘疹，主要发生在颈部的外侧或后部。也有极少报道出现于腋下，背部中央和胸骨上部区域。"},"tr":{"name":"Boynun beyaz fibröz papülozu"}},"xrefs":[{"source":"ICD-10","code":"L98.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EE41.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1989852752"},{"source":"MONDO","code":"0016447","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4706484","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":228221,"name":"Acquired dermis elastic tissue disorder with decreased elastic tissue","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}