raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:213746

Transitional cell carcinoma of the corpus uteri

Synonyms: Endometrial transitional cell carcinoma

Type
Disease
Group
Disorder
Age of onset
Adult
Status
active

A rare uterine cancer characterized by a usually intracavitary, friable, relatively well-circumscribed tumor located in the corpus uteri, with possible infiltration of the myometrium, composed, microscopically, of cells resembling urothelial transition cells, with a papillary or polypoid growth pattern, typically admixed with another type of carcinoma (frequently endometrial adenocarcinoma), generally manifesting with postmenopausal vaginal bleeding.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enTransitional cell carcinoma of the corpus uteriEndometrial transitional cell carcinoma
frCarcinome à cellules transitionnelles du corps de l'utérusCarcinome à cellules transitionnelles de l'endomètre
deTransitionalzellkarzinom des Corpus uteriTransitionalzellkarzinom, endometriales
esCarcinoma de células transicionales de cuerpo de úteroCarcinoma de células transicionales del endometrio
itCarcinoma a cellule transizionali del corpo dell'uteroCarcinoma a cellule transizionali dell'endometrio
nlOvergangscelcarcinoom van corpus uteriEndometriaal overgangscelcarcinoom · Overgangscelcarcinoom van baarmoederlichaam
ptCarcinoma de células de transição do corpo uterino
plRak przejściowokomórkowy trzonu macicyRak przejściowokomórkowy endometrium
csKarcinom těla děložního z přechodných buněkEndometriální karcinom z přechodných buněk
ukПерехідно-клітинна карцинома тіла маткиПерехідно-клітинна карцинома ендометрія
zh子宫体移行细胞癌子宫内膜移行细胞癌
trKorpus uteri'nin geçiş hücreli karsinomuEndometrial geçiş hücreli karsinom

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C54.9BTNTattributedvalidated
ICD-112C76.YNTBTindexvalidated
MONDO0016272Evalidated
UMLSC5191668Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

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Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Annual incidence<1 / 1 000 000—EuropeClass onlyValidatedRARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

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Sources for this card