Transitional cell carcinoma of the corpus uteri
Synonyms: Endometrial transitional cell carcinoma
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adult
- Status
- active
A rare uterine cancer characterized by a usually intracavitary, friable, relatively well-circumscribed tumor located in the corpus uteri, with possible infiltration of the myometrium, composed, microscopically, of cells resembling urothelial transition cells, with a papillary or polypoid growth pattern, typically admixed with another type of carcinoma (frequently endometrial adenocarcinoma), generally manifesting with postmenopausal vaginal bleeding.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Transitional cell carcinoma of the corpus uteri | Endometrial transitional cell carcinoma |
| fr | Carcinome à cellules transitionnelles du corps de l'utérus | Carcinome à cellules transitionnelles de l'endomètre |
| de | Transitionalzellkarzinom des Corpus uteri | Transitionalzellkarzinom, endometriales |
| es | Carcinoma de células transicionales de cuerpo de útero | Carcinoma de células transicionales del endometrio |
| it | Carcinoma a cellule transizionali del corpo dell'utero | Carcinoma a cellule transizionali dell'endometrio |
| nl | Overgangscelcarcinoom van corpus uteri | Endometriaal overgangscelcarcinoom · Overgangscelcarcinoom van baarmoederlichaam |
| pt | Carcinoma de células de transição do corpo uterino | |
| pl | Rak przejściowokomórkowy trzonu macicy | Rak przejściowokomórkowy endometrium |
| cs | Karcinom těla děložního z přechodných buněk | Endometriální karcinom z přechodných buněk |
| uk | Перехідно-клітинна карцинома тіла матки | Перехідно-клітинна карцинома ендометрія |
| zh | 子宫体移行细胞癌 | 子宫内膜移行细胞癌 |
| tr | Korpus uteri'nin geçiş hücreli karsinomu | Endometrial geçiş hücreli karsinom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C54.9 | BTNT | attributed | validated |
| ICD-11 | 2C76.Y | NTBT | index | validated |
| MONDO | 0016272 | E | validated | |
| UMLS | C5191668 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213569Rare cancer of corpus uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | — | Europe | Class only | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213746
- This record as JSON: /data/d/213746.json