raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:213721

Undifferentiated carcinoma of the corpus uteri

Synonyms: Endometrial undifferentiated carcinoma

Type
Disease
Group
Disorder
Status
active

Undifferentiated carcinoma of the corpus uteri is a rare cancer of corpus uteri presenting as a large, polypoid, intraluminal mass with necrosis, composed of small to intermediate-size, relatively uniform, dyshesive cells displaying no differentiation. It usually presents with dysfunctional bleeding or vaginal discharge and, less often, abdominal pain. Association with Lynch syndrome was reported.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enUndifferentiated carcinoma of the corpus uteriEndometrial undifferentiated carcinoma
frCarcinome indifférencié du corps de l'utérusCarcinome indifférencié de l'endomètre
deUndifferenziertes Karzinom des Corpus uteriKarzinom, endometriales undifferenziertes
esCarcinoma indiferenciado de cuerpo uterinoCarcinoma indiferenciado del endometrio
itCarcinoma non differenziato del corpo dell'uteroCarcinoma non differenziato dell'endometrio
nlOngedifferentieerd carcinoom van corpus uteriEndometriaal ongedifferentieerd carcinoom · Ongedifferentieerd carcinoom van baarmoederlichaam · Ongedifferentieerd carcinoom van endometrium
ptCarcinoma indiferenciado do corpo uterino
plNiezróżnicowany rak trzonu macicyNiezróżnicowany rak endometrium
csNediferencovaný karcinom těla děložníhoEndometriální nediferencovaný karcinom
ukНедиференційована карцинома тіла маткиНедиференційована карцинома ендометрія
zh子宫体未分化癌子宫内膜未分化癌
trKorpus uteri'nin farklılaşmamış karsinomuEndometrial farklılaşmamış karsinom

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10C54BTNTspecificvalidated
ICD-10C54.0BTNTspecificvalidated
ICD-10C54.1BTNTspecificvalidated
ICD-10C54.2BTNTspecificvalidated
ICD-10C54.3BTNTspecificvalidated
ICD-10C54.8BTNTspecificvalidated
ICD-112C76.YNTBTindexvalidated
MONDO0016267Evalidated
UMLSC4707822Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card