Undifferentiated carcinoma of the corpus uteri
Synonyms: Endometrial undifferentiated carcinoma
- Type
- Disease
- Group
- Disorder
- Status
- active
Undifferentiated carcinoma of the corpus uteri is a rare cancer of corpus uteri presenting as a large, polypoid, intraluminal mass with necrosis, composed of small to intermediate-size, relatively uniform, dyshesive cells displaying no differentiation. It usually presents with dysfunctional bleeding or vaginal discharge and, less often, abdominal pain. Association with Lynch syndrome was reported.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Undifferentiated carcinoma of the corpus uteri | Endometrial undifferentiated carcinoma |
| fr | Carcinome indifférencié du corps de l'utérus | Carcinome indifférencié de l'endomètre |
| de | Undifferenziertes Karzinom des Corpus uteri | Karzinom, endometriales undifferenziertes |
| es | Carcinoma indiferenciado de cuerpo uterino | Carcinoma indiferenciado del endometrio |
| it | Carcinoma non differenziato del corpo dell'utero | Carcinoma non differenziato dell'endometrio |
| nl | Ongedifferentieerd carcinoom van corpus uteri | Endometriaal ongedifferentieerd carcinoom · Ongedifferentieerd carcinoom van baarmoederlichaam · Ongedifferentieerd carcinoom van endometrium |
| pt | Carcinoma indiferenciado do corpo uterino | |
| pl | Niezróżnicowany rak trzonu macicy | Niezróżnicowany rak endometrium |
| cs | Nediferencovaný karcinom těla děložního | Endometriální nediferencovaný karcinom |
| uk | Недиференційована карцинома тіла матки | Недиференційована карцинома ендометрія |
| zh | 子宫体未分化癌 | 子宫内膜未分化癌 |
| tr | Korpus uteri'nin farklılaşmamış karsinomu | Endometrial farklılaşmamış karsinom |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C54 | BTNT | specific | validated |
| ICD-10 | C54.0 | BTNT | specific | validated |
| ICD-10 | C54.1 | BTNT | specific | validated |
| ICD-10 | C54.2 | BTNT | specific | validated |
| ICD-10 | C54.3 | BTNT | specific | validated |
| ICD-10 | C54.8 | BTNT | specific | validated |
| ICD-11 | 2C76.Y | NTBT | index | validated |
| MONDO | 0016267 | E | validated | |
| UMLS | C4707822 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213569Rare cancer of corpus uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213721
- This record as JSON: /data/d/213721.json