Adenosarcoma of the corpus uteri
- Type
- Disease
- Group
- Disorder
- Status
- active
A rare subtype of mixed epithelial-mesenchymal tumor, often presenting as a large, exophytic polypoid lesion, which may extend through the cervix, composed of benign or atypical epithelium and low-grade malignant stroma. It usually presents with dysfunctional bleeding or vaginal discharge and less often abdominal pain. Association with long-term unopposed estrogen therapy, tamoxifen therapy and a history of pelvic radiation has been reported.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Adenosarcoma of the corpus uteri | |
| fr | Adénosarcome du corps de l'utérus | |
| de | Adenosarkom des Corpus uteri | |
| es | Adenosarcoma de cuerpo uterino | |
| it | Adenosarcoma del corpo dell'utero | |
| nl | Adenosarcoom van baarmoederlichaam | Adenosarcoom van corpus uteri |
| pt | Adenossarcoma do corpo uterino | |
| pl | Gruczolakomięsak trzonu macicy | |
| cs | Adenosarkom těla děložního | |
| uk | Аденосаркома тіла матки | |
| zh | 子宫体腺肉瘤 | |
| tr | Korpus uteri adenosarkomu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C54.2 | BTNT | attributed | validated |
| ICD-11 | 2B5D.1 | NTBT | index | validated |
| MONDO | 0002878 | E | validated | |
| UMLS | C4707554 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:213589Malignant mixed epithelial and mesenchymal tumor of corpus uteri
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213600
- This record as JSON: /data/d/213600.json