ORPHA:213557

Salivary gland type cancer of the breast

Synonyms: Salivary gland type carcinoma of the breast

Type: Disease
Group: Disorder
Age of onset: Adult
Status: active

Salivary gland type cancer of the breast describes a group of uncommon neoplasms, usually seen in the salivary glands but occurring in the breast, with a variable clinicopathologic spectrum and divided into those with myoepithelial differentiation and those without. This group includes mammary adenoid cystic carcinoma, adenoid cystic carcinoma, mucoepidermoid carcinoma, acinic cell carcinoma, polymorphous low-grade adenocarcinoma and oncocytic carcinoma.

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Salivary gland type cancer of the breast	Salivary gland type carcinoma of the breast
fr	Cancer du sein type glande salivaire	Carcinome du sein type glande salivaire
de	Mammatumor vom Speicheldrüsentyp	Mammakarzinom vom Speicheldrüsentyp
es	Cáncer de mama tipo glándula salivar	Carcinoma de mama tipo glándula salivar
it	Cancro della mammella, tipo ghiandola salivare	Carcinoma della mammella, tipo ghiandola salivare
nl	Speekselklier-type kanker van borst	Speekselklier-type carcinoom van borst
pt	Cancro da mama, tipo glândula salivar
pl	Rak piersi typu śliniankowego	= en
cs	Adenoidně cystický karcinom prsu	= en
uk	Рак молочної залози слинного типу	Карцинома молочної залози слинного типу
zh	唾液腺型乳腺癌	唾液腺型乳腺癌
tr	Memenin tükürük bezi tipi kanseri	Memenin tükrük bezi tipi karsinomu

Definition in:

Cross-references

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	C50.0	BTNT	attributed	validated
ICD-10	C50.1	BTNT	attributed	validated
ICD-10	C50.2	BTNT	attributed	validated
ICD-10	C50.3	BTNT	attributed	validated
ICD-10	C50.4	BTNT	attributed	validated
ICD-10	C50.5	BTNT	attributed	validated
ICD-10	C50.6	BTNT	attributed	validated
ICD-10	C50.8	BTNT	attributed	validated
ICD-11	2C60	NTBT	index	validated
MONDO	0100508	E		validated
UMLS	C4274421	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Classification

Preferential parent (Orphanet linearisation):

ORPHA:250908Rare neoplastic disease

Parents in the classifications (1):

ORPHA:180257Rare malignant breast tumor
rare neoplastic diseases; rare gynecological and obstetric diseases

No children.

Genes

0 direct

Orphanet records no gene directly on this code.

Prevalence and incidence

23 records

Type	Class	Value	Area	Qualification	Validation	Source
Annual incidence	<1 / 1 000 000	0.05 / 100 000	Europe	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.038 / 100 000	Austria	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.095 / 100 000	Belgium	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.024 / 100 000	Bulgaria	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.014 / 100 000	Croatia	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.068 / 100 000	Czech Republic	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.024 / 100 000	Finland	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.077 / 100 000	Germany	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.037 / 100 000	Ireland	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.075 / 100 000	Italy	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.043 / 100 000	Latvia	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.017 / 100 000	Lithuania	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.031 / 100 000	Malta	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.06 / 100 000	Norway	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.013 / 100 000	Poland	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.039 / 100 000	Portugal	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.019 / 100 000	Slovakia	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.044 / 100 000	Slovenia	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.054 / 100 000	Spain	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.09 / 100 000	Switzerland	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.064 / 100 000	Netherlands	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	<1 / 1 000 000	0.053 / 100 000	United Kingdom	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]
Annual incidence	1-9 / 1 000 000	0.323 / 100 000	Estonia	Value and class	Validated	RARECARE surveillance of rare cancers in Europe[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

Sources for this card

Orphanet page: orpha.net/en/disease/detail/213557
This record as JSON: /data/d/213557.json