{"orpha":213557,"name":"Salivary gland type cancer of the breast","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Salivary gland type carcinoma of the breast"],"definition":"Salivary gland type cancer of the breast describes a group of uncommon neoplasms, usually seen in the salivary glands but occurring in the breast, with a variable clinicopathologic spectrum and divided into those with myoepithelial differentiation and those without. This group includes mammary adenoid cystic carcinoma, adenoid cystic carcinoma, mucoepidermoid carcinoma, acinic cell carcinoma, polymorphous low-grade adenocarcinoma and oncocytic carcinoma.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-213557/","orphanet_url":"https://www.orpha.net/en/disease/detail/213557","names":{"fr":{"name":"Cancer du sein type glande salivaire","synonyms":["Carcinome du sein type glande salivaire"],"definition":"Le cancer du sein type glande salivaire décrit un groupe de néoplasmes rares observés habituellement dans les glandes salivaires, mais survenant dans le sein, avec un spectre clinicopathologique variable. Il comprend des néoplasmes avec et sans différenciation myoépithéliale. Ce groupe inclut le carcinome adenoïde kystique, le carcinome muco-épidermoïde, le carcinome à cellules acineuses, l'adénocarcinome polymorphe de bas grade et le carcinome oncocytaire."},"de":{"name":"Mammatumor vom Speicheldrüsentyp","synonyms":["Mammakarzinom vom Speicheldrüsentyp"]},"es":{"name":"Cáncer de mama tipo glándula salivar","synonyms":["Carcinoma de mama tipo glándula salivar"],"definition":"El cáncer de mama tipo glándula salivar describe un grupo de neoplasias desconocidas, normalmente vistas en las glándulas salivares pero que aparecen en la mama, con un espectro clínico patológico variable y dividido en aquellos con o sin diferenciación mioepitelial. Este grupo incluye el carcinoma adenoide quístico (consulte este término), el carcinoma mucoepidermoide, el carcinoma de células acinares, el adenocarcinoma polimorfo de grado bajo y el carcinoma oncocítico."},"it":{"name":"Cancro della mammella, tipo ghiandola salivare","synonyms":["Carcinoma della mammella, tipo ghiandola salivare"]},"nl":{"name":"Speekselklier-type kanker van borst","synonyms":["Speekselklier-type carcinoom van borst"],"definition":"Speekselklier-type kanker van de borst beschrijft een groep ongewone neoplasma's die normaal worden waargenomen in de speekselklieren maar voorkomen in de borst. Deze neoplasma's hebben een variabel klinisch-pathologisch spectrum en worden verdeeld op basis van het al dan niet aanwezig zijn van myoepitheliale differentiatie. Deze groep omvat adenoïd cystisch carcinoom van de borst, adenoïd cystisch carcinoom (zie deze term), mucoepidermoïd carcinoom, acinaire celcarcinoom, polymorf laaggradig adenocarcinoom en oncocytisch carcinoom."},"pt":{"name":"Cancro da mama, tipo glândula salivar"},"pl":{"name":"Rak piersi typu śliniankowego","synonyms":["Salivary gland type carcinoma of the breast"]},"cs":{"name":"Adenoidně cystický karcinom prsu","synonyms":["Salivary gland type carcinoma of the breast"]},"uk":{"name":"Рак молочної залози слинного типу","synonyms":["Карцинома молочної залози слинного типу"],"definition":"Salivary gland type cancer of the breast describes a group of uncommon neoplasms, usually seen in the salivary glands but occurring in the breast, with a variable clinicopathologic spectrum and divided into those with myoepithelial differentiation and those without. This group includes mammary adenoid cystic carcinoma, adenoid cystic carcinoma (see this term), mucoepidermoid carcinoma, acinic cell carcinoma, polymorphous low-grade adenocarcinoma and oncocytic carcinoma."},"zh":{"name":"唾液腺型乳腺癌","synonyms":["唾液腺型乳腺癌"],"definition":"唾液腺型乳腺癌是一组发生于乳腺的罕见肿瘤，常见于唾液腺，可根据不同的临床病理特征分为以下2类：肌上皮分化型和非上皮型。这一组包括乳腺腺样囊性癌、腺样囊腺癌（见该术语）、黏液表皮样癌，腺泡细胞癌、多形低度腺癌和嗜酸细胞癌。"},"tr":{"name":"Memenin tükürük bezi tipi kanseri","synonyms":["Memenin tükrük bezi tipi karsinomu"]}},"xrefs":[{"source":"ICD-10","code":"C50.0","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C50.1","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C50.2","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C50.3","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C50.4","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C50.5","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C50.6","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-10","code":"C50.8","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2C60","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"2145246967"},{"source":"MONDO","code":"0100508","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4274421","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":180257,"name":"Rare malignant breast tumor","classifications":[202,205]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.05,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.038,"area":"Austria","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.095,"area":"Belgium","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.024,"area":"Bulgaria","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.014,"area":"Croatia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.068,"area":"Czech Republic","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.024,"area":"Finland","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.077,"area":"Germany","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.037,"area":"Ireland","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.075,"area":"Italy","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.043,"area":"Latvia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.017,"area":"Lithuania","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.031,"area":"Malta","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.06,"area":"Norway","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.013,"area":"Poland","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.039,"area":"Portugal","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.019,"area":"Slovakia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.044,"area":"Slovenia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.054,"area":"Spain","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.09,"area":"Switzerland","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.064,"area":"Netherlands","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.053,"area":"United Kingdom","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.323,"area":"Estonia","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}