Malignant mixed Müllerian tumor of the ovary
Synonyms: MMMT of the ovary · Ovarian carcinosarcoma · Ovarian malignant mixed Müllerian tumor · Ovarian malignant mixed epithelial mesenchymal tumor
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adult
- Status
- active
Malignant mixed Müllerian tumor of the ovary is a rare and very aggressive neoplasm presenting most commonly in postmenopausal women and is composed of adenocarcinomatous and sarcomatous elements and, depending on the types of these elements, can be classified as homologous or heterologous. It often has a poor prognosis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Malignant mixed Müllerian tumor of the ovary | MMMT of the ovary · Ovarian carcinosarcoma · Ovarian malignant mixed Müllerian tumor · Ovarian malignant mixed epithelial mesenchymal tumor |
| fr | Tumeur maligne mixte müllérienne de l'ovaire | Carcinosarcome de l'ovaire · MMMT de l'ovaire |
| de | Maligner Müllerscher Mischtumor des Ovars | Gemischte epitheliale und mesenchymale Tumoren des Ovars · Karzinosarkom des Ovars · MMMT des Ovars |
| es | Tumor mülleriano mixto maligno de ovario | Carcinosarcoma ovárico · TMMM del ovario · Tumor ovárico maligno mixto epitelial y mesenquimatoso · Tumor ovárico mülleriano mixto maligno |
| it | Tumore misto maligno mesenchimale ed epiteliale dell'ovaio | Carcinosarcoma dell'ovaio |
| nl | Maligne mengtumor van Müller van ovarium | MMMT van het ovarium · Maligne mengtumor van Müller van eierstok · Ovarieel carcinosarcoom · Ovariële maligne gemengde epitheliale mesenchymale tumor · Ovariële maligne mengtumor van Müller |
| pt | Tumor maligno mesenquimatoso e epitelial misto do ovário | |
| pl | Złośliwy mieszany guz jajnika z przewodów Mullera | Mięsakorak jajnika · Złośliwy mieszany guz jajnika z nabłonka mezenchymalego |
| cs | Maligní mesenchymální nádor ovaria | Ovariální karcinosarkom |
| uk | Злоякісна змішана мюллерова пухлина яєчника | МММТ яєчника · Карциносаркома яєчників · Злоякісна змішана епітеліальна мезенхімальна пухлина яєчника · Злоякісна змішана мюллерова пухлина яєчників |
| zh | 卵巢恶性混合性苗勒管瘤 | 卵巢恶性混合性上皮间质瘤 |
| tr | Yumurtalıkta habis karma M³llerian tümörü | Overin MMMT'si · Overin karsinosarkomu · Overin habis karma Müllerian tümörü · Overin habis karma epitel mezenkimal tümörü |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C56 | NTBT | attributed | validated |
| ICD-11 | 2B5D.0 | E | specific | validated |
| MONDO | 0003792 | E | validated | |
| UMLS | C0392998 | E | validated | |
| GARD | 7296 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:398934Malignant epithelial tumor of ovary
rare neoplastic diseases; rare gynecological and obstetric diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-9 / 1 000 000 | 0.12 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/213512
- This record as JSON: /data/d/213512.json