Spindle cell hemangioma
Synonyms: Spindle cell haemangioma · Spindle cell hemangioendothelioma
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- Adolescent, Adult, Childhood, Elderly
- Status
- active
Spindle cell hemangioma (SCH), also known as spindle cell hemangioendothelioma, is a rare benign vascular tumor either solitary or multiple, characterized by cavernous blood vessels separated by spindle cells reminiscent of those in Kaposis sarcoma and located in the dermis and subcutis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Spindle cell hemangioma | Spindle cell haemangioma · Spindle cell hemangioendothelioma |
| fr | Hémangiome à cellules fusiformes | Hémangioendothéliome à cellules fusiformes |
| de | Spindelzell-Hämangiom | Spindelzell-Hämangioendotheliom |
| es | Hemangioma de células fusiformes | Hemangioendotelioma de células fusiformes · Hemangioma fusocelular |
| it | Emangioma a cellule fusiformi | Emangioendotelioma a cellule fusiformi |
| nl | Spoelcelhemangioom | Spoelcelhemangio-endothelioom |
| pt | Hemangioma de células fusiformes | |
| pl | Naczyniak wrzecionowatokomórkowy | Śródbłoniak nabłonkowaty wrzecionowatokomórkowy |
| cs | Vřetenobuněčný hemangiom | Vřetenobuněčný hemangioendoteliom |
| uk | Веретеноклітинна гемангіома | Веретеноклітинна гемангіоендотеліома |
| zh | 梭形细胞血管瘤 | 梭形细胞血管内皮瘤 |
| tr | Mil hücre hemanjiyomu | Mil hücreli hemanjioendotelyoma |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | D18.0 | NTBT | attributed | validated |
| ICD-11 | 2F2Y | NTBT | index | validated |
| ICD-11 | XH6RP8 | E | specific | validated |
| MONDO | 0016222 | E | validated | |
| UMLS | C1304508 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:673470Benign vascular tumor
rare developmental anomalies during embryogenesis; rare circulatory system diseases; rare neoplastic diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | Unknown | — | Worldwide | Class only | Validated | WHO Classification of Tumours[OTHER] |
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | WHO Classification of Tumours[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/210584
- This record as JSON: /data/d/210584.json