{"orpha":210584,"name":"Spindle cell hemangioma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Spindle cell haemangioma","Spindle cell hemangioendothelioma"],"definition":"Spindle cell hemangioma (SCH), also known as spindle cell hemangioendothelioma, is a rare benign vascular tumor either solitary or multiple, characterized by cavernous blood vessels separated by spindle cells reminiscent of those in Kaposi’s sarcoma and located in the dermis and subcutis.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-210584/","orphanet_url":"https://www.orpha.net/en/disease/detail/210584","names":{"fr":{"name":"Hémangiome à cellules fusiformes","synonyms":["Hémangioendothéliome à cellules fusiformes"],"definition":"Tumeur vasculaire bénigne rare, unique ou multiple, également connue sous le nom d'hémangioendothéliome à cellules fusiformes, caractérisée par des vaisseaux sanguins caverneux séparés par des cellules fusiformes ressemblant à celles du sarcome de Kaposi et situées dans le derme et l'hypoderme."},"de":{"name":"Spindelzell-Hämangiom","synonyms":["Spindelzell-Hämangioendotheliom"],"definition":"Das Spindelzell-Hämangiom (SCH), auch Spindelzell-Hämangio-Endotheliom genannt, ist ein seltener gutartiger, entweder solitär oder multipel auftretender Gefäßtumor der Dermis und Subkutis mit kavernösen Blutgefäßen, die durch Spindelzellen, ähnlich denen des Kaposi-Sarkoms, getrennt sind"},"es":{"name":"Hemangioma de células fusiformes","synonyms":["Hemangioendotelioma de células fusiformes","Hemangioma fusocelular"],"definition":"El hemangioma de células fusiformes (SCH), también conocido como hemangioendotelioma de células fusiformes, es un tumor vascular benigno raro solitario o múltiple, que se caracteriza por vasos sanguíneos cavernosos separados por células fusiformes que recuerdan a las del sarcoma de Kaposi y que están localizadas en la dermis y en el tejido subcutáneo."},"it":{"name":"Emangioma a cellule fusiformi","synonyms":["Emangioendotelioma a cellule fusiformi"],"definition":"L'emangioma a cellule fusiformi (SCH), o emangioendotelioma a cellule fusiformi, è un tumore vascolare benigno raro, solitario o multiplo, caratterizzato da vasi sanguigni cavernosi separati da cellule fusiformi che ricordano quelle del sarcoma di Kaposi, localizzate nel derma e nel tessuto sottocutaneo"},"nl":{"name":"Spoelcelhemangioom","synonyms":["Spoelcelhemangio-endothelioom"],"definition":"Een zeldzame goedaardige vasculaire, hetzij solitaire hetzij meervoudige, tumor, ook gekend als spoelcelhemangio-endothelioom, gekenmerkt door caverneuze bloedvaten gescheiden door spoelcellen die lijken op die van Kaposi-sarcoom en gesitueerd zijn in dermis en subcutis."},"pt":{"name":"Hemangioma de células fusiformes"},"pl":{"name":"Naczyniak wrzecionowatokomórkowy","synonyms":["Śródbłoniak nabłonkowaty wrzecionowatokomórkowy"]},"cs":{"name":"Vřetenobuněčný hemangiom","synonyms":["Vřetenobuněčný hemangioendoteliom"]},"uk":{"name":"Веретеноклітинна гемангіома","synonyms":["Веретеноклітинна гемангіоендотеліома"],"definition":"Spindle cell hemangioma (SCH), also known as spindle cell hemangioendothelioma, is a rare benign vascular tumor either solitary or multiple, characterized by cavernous blood vessels separated by spindle cells reminiscent of those in Kaposi’s sarcoma and located in the dermis and subcutis."},"zh":{"name":"梭形细胞血管瘤","synonyms":["梭形细胞血管内皮瘤"],"definition":"梭形细胞血管瘤（SCH）又称梭形细胞血管内皮瘤，是一种罕见的良性血管瘤，其特征为海绵状血管被梭形细胞分隔，类似于真皮和皮下的卡波西肉瘤。"},"tr":{"name":"Mil hücre hemanjiyomu","synonyms":["Mil hücreli hemanjioendotelyoma"]}},"xrefs":[{"source":"ICD-10","code":"D18.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F2Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1044935023"},{"source":"ICD-11","code":"XH6RP8","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1579636498"},{"source":"MONDO","code":"0016222","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1304508","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":673470,"name":"Benign vascular tumor","classifications":[147,198,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adolescent","Adult","Childhood","Elderly"],"prevalence":[{"type":"Annual incidence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"WHO Classification of Tumours[OTHER]"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"WHO Classification of Tumours[OTHER]"}],"phenotypes":null}