Neurolymphomatosis
- Type
- Disease
- Group
- Disorder
- Status
- active
Neurolymphomatosis is a rare syndrome of peripheral and cranial nerve dysfunction in patients with hematologic malignancies, mostly non-Hodgkin's lymphoma or acute leukemia, characterized by painful or painless involvement of peripheral or cranial nerves or nerve roots. The clinical presentation is diverse depending on the site involved and includes plexopathy, mononeuritis multiplex, peripheral neuropathy, radiculopathy and cranial nerve palsies.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Neurolymphomatosis | |
| fr | Neurolymphomatose | |
| de | Neurolymphomatose | |
| es | Neurolinfomatosis | |
| it | Neurolinfomatosi | |
| nl | Neurolymfomatose | |
| pt | Neurolinfomatose | |
| pl | Neurolimfomatoza | |
| cs | Neurolymfomatóza | |
| uk | Нейролімфоматоз | |
| zh | 神经鞘瘤病 | |
| tr | Nörolenfomatoz |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C96.7 | NTBT | attributed | not yet validated |
| ICD-10 | G63.1 | NTBT | attributed | not yet validated |
| ICD-11 | 8C01.Y | NTBT | index | validated |
| MONDO | 0016101 | E | validated | |
| MeSH | D000077162 | E | validated | |
| UMLS | C4553088 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:207046Malignant lymphoma with peripheral neuropathy
rare neurological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/206586
- This record as JSON: /data/d/206586.json