raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:1850

Renal dysplasia-megalocystis-sirenomelia syndrome

inactive · moved to ORPHA:1768Familial caudal dysgenesis

Synonyms: Selig-Benacerraf-Greene syndrome

Type
Malformation syndrome
Group
Disorder
Status
inactive
Flag
Deprecated entity

This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Familial caudal dysgenesis

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRenal dysplasia-megalocystis-sirenomelia syndromeSelig-Benacerraf-Greene syndrome
frSyndrome de dysplasie rénale-mégavessie-sirénomelieSyndrome de Selig-Benacerraf-Greene
deNierendysplasie-Megazystis-Sirenomelie-SyndromSelig-Benacerraf-Greene-Syndrom
esSíndrome de displasia renal-megacistis-sirenomeliaSíndrome de Selig-Benacerraf-Greene
itSindrome displasia renale-megalocisti-sirenomeliaSindrome di Selig-Benacerraf-Greene
nlRenale dysplasie - megalocyste - sirenomelie-syndroomSyndroom van Selig-Benacerraf-Greene
ptSíndrome de displasia renal-megacistis-sirenomeliaSíndrome Selig-Benacerraf-Greene
plZespół dysplazji nerek, pęcherza moczowego olbrzymiego i syrenomeliiZespół Seliga, Benacerrafa i Greene
csSyndrom zahrnující renální dysplázii, megalocytózu a sirenomeliiSeligův-Benacerrafův-Greeneho syndrom · Selig-Benacerraf-Greeneho syndrom
ukСиндром ниркової дисплазії-мегалоцистозу-сиреномеліїСиндром Селіга-Бенасеррафа-Гріна
zh肾发育不良-巨膀胱-并腿畸形综合征Selig-Benacerraf-Greene综合征
trBöbrek displazisi-megalosistis-sirenomelia sendromuSelig-Benacerraf-Greene sendromu
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card