{"orpha":1850,"name":"Renal dysplasia-megalocystis-sirenomelia syndrome","type":"Malformation syndrome","group":"Disorder","status":"inactive","flags":["Deprecated entity"],"synonyms":["Selig-Benacerraf-Greene syndrome"],"definition":null,"note":"This entity has been excluded from the Orphanet nomenclature of rare diseases and moved to Familial caudal dysgenesis","url":"https://raremap.alftech.space/d/ORPHA-1850/","orphanet_url":"https://www.orpha.net/en/disease/detail/1850","names":{"fr":{"name":"Syndrome de dysplasie rénale-mégavessie-sirénomelie","synonyms":["Syndrome de Selig-Benacerraf-Greene"]},"de":{"name":"Nierendysplasie-Megazystis-Sirenomelie-Syndrom","synonyms":["Selig-Benacerraf-Greene-Syndrom"]},"es":{"name":"Síndrome de displasia renal-megacistis-sirenomelia","synonyms":["Síndrome de Selig-Benacerraf-Greene"]},"it":{"name":"Sindrome displasia renale-megalocisti-sirenomelia","synonyms":["Sindrome di Selig-Benacerraf-Greene"]},"nl":{"name":"Renale dysplasie - megalocyste - sirenomelie-syndroom","synonyms":["Syndroom van Selig-Benacerraf-Greene"]},"pt":{"name":"Síndrome de displasia renal-megacistis-sirenomelia","synonyms":["Síndrome Selig-Benacerraf-Greene"]},"pl":{"name":"Zespół dysplazji nerek, pęcherza moczowego olbrzymiego i syrenomelii","synonyms":["Zespół Seliga, Benacerrafa i Greene"]},"cs":{"name":"Syndrom zahrnující renální dysplázii, megalocytózu a sirenomelii","synonyms":["Seligův-Benacerrafův-Greeneho syndrom","Selig-Benacerraf-Greeneho syndrom"]},"uk":{"name":"Синдром ниркової дисплазії-мегалоцистозу-сиреномелії","synonyms":["Синдром Селіга-Бенасеррафа-Гріна"]},"zh":{"name":"肾发育不良-巨膀胱-并腿畸形综合征","synonyms":["Selig-Benacerraf-Greene综合征"]},"tr":{"name":"Böbrek displazisi-megalosistis-sirenomelia sendromu","synonyms":["Selig-Benacerraf-Greene sendromu"]}},"xrefs":[],"associations":[{"type":"Moved to","orpha":1768,"name":"Familial caudal dysgenesis"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}