raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:181371

Rare diabetes mellitus type 1

Synonyms: Rare insulin-dependent diabetes mellitus

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enRare diabetes mellitus type 1Rare insulin-dependent diabetes mellitus
frForme rare de diabète de type 1Forme rare de diabète sucré de type 1 · Forme rare de diabète sucré insulino-dépendant
deSeltener Diabetes mellitus Typ 1Insulinabhängiger Diabetes mellitus, seltene Form
esDiabetes mellitus rara tipo 1Diabetes mellitus insulinodependiente rara
itDiabete mellito raro, tipo 1Diabete mellito insulina-dipendente raro
nlZeldzame diabetes mellitus type 1Zeldzame insuline-afhankelijke diabetes mellitus
ptDiabetes mellitus insulino-dependente, raros
plRzadka odmiana cukrzycy typu 1Rzadka odmiana cukrzycy insulinozależnej
csVzácný diabetes mellitus 1. typuVzácný inzulin-dependentní diabetes mellitus
ukРідкісний цукровий діабет, тип 1Рідкісний інсулінозалежний цукровий діабет
zh罕见1型糖尿病罕见胰岛素依赖型糖尿病
trNadir görülen diabetes mellitus tip 1Nadir insülin-bağımlı diabetes mellitus
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO15886Evalidated
UMLSC5679586Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (5):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card