raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:178554

Aggressive primary cutaneous B-cell lymphoma

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAggressive primary cutaneous B-cell lymphoma
frLymphome B cutané primitif d'évolution agressive
dePrimär kutanes B-Zell-Lymphom, aggressives
esLinfoma cutáneo primario de células B agresivo
itLinfoma cutaneo primitivo aggressivo a cellule B
nlAgressief primair cutaan B-cellymfoom
ptLinfoma cutâneo de células B, agressivo
plPierwotny skórny chłoniak agresywny B-komórkowy
csPrimární kožní B-buněčný lymfom s agresivním průběhemPrimární kožní agresivní B-buněčný lymfom
ukАгресивна первинна шкірна В-клітинна лімфома
zh侵袭性性原发性皮肤B细胞淋巴瘤
trAgresif primer kutanöz B hücreli lenfoma
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO15818Evalidated
UMLSC5680500Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (2):

Children (1):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card