{"orpha":178554,"name":"Aggressive primary cutaneous B-cell lymphoma","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-178554/","orphanet_url":"https://www.orpha.net/en/disease/detail/178554","names":{"fr":{"name":"Lymphome B cutané primitif d'évolution agressive"},"de":{"name":"Primär kutanes B-Zell-Lymphom, aggressives"},"es":{"name":"Linfoma cutáneo primario de células B agresivo"},"it":{"name":"Linfoma cutaneo primitivo aggressivo a cellule B"},"nl":{"name":"Agressief primair cutaan B-cellymfoom"},"pt":{"name":"Linfoma cutâneo de células B, agressivo"},"pl":{"name":"Pierwotny skórny chłoniak agresywny B-komórkowy"},"cs":{"name":"Primární kožní B-buněčný lymfom s agresivním průběhem","synonyms":["Primární kožní agresivní B-buněčný lymfom"]},"uk":{"name":"Агресивна первинна шкірна В-клітинна лімфома"},"zh":{"name":"侵袭性性原发性皮肤B细胞淋巴瘤"},"tr":{"name":"Agresif primer kutanöz B hücreli lenfoma"}},"xrefs":[{"source":"MONDO","code":"15818","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680500","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":300846,"name":"Aggressive B-cell non-Hodgkin lymphoma","classifications":[194,202,233]},{"orpha":178563,"name":"Primary cutaneous B-cell lymphoma","classifications":[187,194,202,233]}],"children":[{"orpha":178544,"name":"Primary cutaneous diffuse large B-cell lymphoma, leg type","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}