ORPHA:178551
Aggressive primary cutaneous T-cell lymphoma
- Type
- Clinical group
- Group
- Group of disorders
- Status
- active
This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Aggressive primary cutaneous T-cell lymphoma | |
| fr | Lymphome T cutané primitif d'évolution agressive | |
| de | Primär kutanes T-Zell-Lymphom, aggressives | |
| es | Linfoma cutáneo primario de células T agresivo | |
| it | Linfoma cutaneo primitivo aggressivo a cellule T | |
| nl | Agressief primair cutaan T-cellymfoom | |
| pt | Linfoma cutâneo de células T, agressivo | |
| pl | Pierwotny skórny chłoniak agresywny T-komórkowy | |
| cs | Primární kožní T-buněčný lymfom s agresivním průběhem | Primární kožní agresivní T-buněčný lymfom |
| uk | Агресивна первинна шкірна Т-клітинна лімфома | |
| zh | 侵袭性性原发性皮肤T细胞淋巴瘤 | |
| tr | Agresif primer kutanöz T hücreli lenfoma |
2
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| MONDO | 15817 | E | validated | |
| UMLS | C5680497 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:171901Primary cutaneous T-cell lymphoma
rare skin diseases; rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
Children (6):
- ORPHA:86875Adult T-cell leukemia/lymphoma
- ORPHA:86879Extranodal nasal NK/T cell lymphoma
- ORPHA:178528Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma
- ORPHA:178533Primary cutaneous gamma/delta-positive T-cell lymphoma
- ORPHA:86885Primary cutaneous peripheral T-cell lymphoma not otherwise specified
- ORPHA:3162Sézary syndrome
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/178551
- This record as JSON: /data/d/178551.json