{"orpha":178551,"name":"Aggressive primary cutaneous T-cell lymphoma","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-178551/","orphanet_url":"https://www.orpha.net/en/disease/detail/178551","names":{"fr":{"name":"Lymphome T cutané primitif d'évolution agressive"},"de":{"name":"Primär kutanes T-Zell-Lymphom, aggressives"},"es":{"name":"Linfoma cutáneo primario de células T agresivo"},"it":{"name":"Linfoma cutaneo primitivo aggressivo a cellule T"},"nl":{"name":"Agressief primair cutaan T-cellymfoom"},"pt":{"name":"Linfoma cutâneo de células T, agressivo"},"pl":{"name":"Pierwotny skórny chłoniak agresywny T-komórkowy"},"cs":{"name":"Primární kožní T-buněčný lymfom s agresivním průběhem","synonyms":["Primární kožní agresivní T-buněčný lymfom"]},"uk":{"name":"Агресивна первинна шкірна Т-клітинна лімфома"},"zh":{"name":"侵袭性性原发性皮肤T细胞淋巴瘤"},"tr":{"name":"Agresif primer kutanöz T hücreli lenfoma"}},"xrefs":[{"source":"MONDO","code":"15817","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680497","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":171901,"name":"Primary cutaneous T-cell lymphoma","classifications":[187,194,202,233]}],"children":[{"orpha":86875,"name":"Adult T-cell leukemia/lymphoma","type":"Disease"},{"orpha":86879,"name":"Extranodal nasal NK/T cell lymphoma","type":"Disease"},{"orpha":178528,"name":"Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma","type":"Disease"},{"orpha":178533,"name":"Primary cutaneous gamma/delta-positive T-cell lymphoma","type":"Disease"},{"orpha":86885,"name":"Primary cutaneous peripheral T-cell lymphoma not otherwise specified","type":"Disease"},{"orpha":3162,"name":"Sézary syndrome","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}