Composite lymphoma
Synonyms: Composite Hodgkin and non-Hodgkin lymphoma
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adult, Elderly
- Status
- active
A rare lymphoma characterized by the concurrent occurrence of two or more histologic types of lymphoma involving the same anatomic site. Composite lymphomas can be combinations of two non-Hodgkin lymphomas or of a non-Hodgkin and a Hodgkin lymphoma. In many cases, the tumors are clonally related. Clinical presentation and treatment are determined by the more aggressive component.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Composite lymphoma | Composite Hodgkin and non-Hodgkin lymphoma |
| fr | Lymphome composite | Lymphome composite Hodgkinien et non Hodgkinien |
| de | Komposit-Lymphom | Kombinationslymphom von HL und Non-HL |
| es | Linfoma compuesto | Linfoma Hodgkin y no Hodgkin compuesto · Linfoma de Hodgkin y no Hodgkin compuesto |
| it | Linfoma composito | Linfoma composito di Hodgkin e non-Hodgkin |
| nl | Samengesteld lymfoom | Samengesteld Hodgkin- en non-Hodgkin-lymfoom |
| pt | Linfoma composto | |
| pl | Chłoniak mieszany | Chłoniak mieszany Hodgkina i non-Hodgkin |
| cs | Kompozitní lymfom | Kompozitní Hodgkinův a non-Hodgkinův lymfom |
| uk | Композитна лімфома | Комбінована лімфома Ходжкіна та неходжкінська лімфома |
| zh | 复合淋巴瘤 | 复合霍奇金和非霍奇金淋巴瘤 |
| tr | Kompozit lenfoma | Kompozit Hodgkin ve Hodgkin olmayan lenfoma |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C81.7 | NTBT | attributed | validated |
| ICD-10 | C85.7 | NTBT | attributed | validated |
| ICD-11 | XH3BP6 | NTBT | index | validated |
| MONDO | 0005710 | E | validated | |
| MeSH | D058617 | E | validated | |
| UMLS | C0545080 | E | validated | |
| MedDRA | 10073957 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:223735Lymphoma
rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | <1 / 1 000 000 | 0.01 / 100 000 | Europe | Value and class | Validated | RARECARE surveillance of rare cancers in Europe[OTHER] |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/168966
- This record as JSON: /data/d/168966.json