ORPHA:168816
Peritoneal inclusion cyst
Synonyms: Benign multicystic peritoneal mesothelioma · Multicystic mesothelioma · Multilocular peritoneal inclusion cyst · Peritoneal cyctic mesothelioma
- Type
- Disease
- Group
- Disorder
- Inheritance
- Unknown
- Age of onset
- Adult
- Status
- active
Peritoneal cystic mesothelioma is a rare benign tumor characterized by the formation of intra-abdominal multilocular cystic masses.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Peritoneal inclusion cyst | Benign multicystic peritoneal mesothelioma · Multicystic mesothelioma · Multilocular peritoneal inclusion cyst · Peritoneal cyctic mesothelioma |
| fr | Kyste d'inclusion péritonéale | Kyste à inclusion péritonéal multiloculaire · Mésothéliome multikystique · Mésothéliome péritonéal multikystique bénin |
| de | Peritoneale Inklusionszyste | Inklusionszyste, multilokuläre peritoneale · Mesotheliom, benignes mulitzystisches peritoneales · Mesotheliom, multizystisches · Peritonealmesotheliom, zystisches |
| es | Quiste de inclusión peritoneal | Mesotelioma multiquístico · Mesotelioma peritoneal multiquístico benigno · Mesotelioma peritoneal quístico · Quiste de inclusión peritoneal multilocular |
| it | Cisti da inclusione peritoneale | Cisti peritoneale multioculare da inclusione · Mesotelioma multicistico · Mesotelioma peritoneale multicistico benigno · Mesotelioma cistico peritoneale |
| nl | Peritoneale inclusiecyste | Goedaardig multicystisch peritoneaal mesothelioom · Multicystisch mesothelioom · Multiloculaire peritoneale inclusiecyste · Peritoneaal cystisch mesothelioom |
| pt | Quisto de inclusão peritoneal | Mesotelioma multiquístico · Mesotelioma peritoneal multiquistico benigno · Mesotelioma quistico peritoneal · Quisto de inclusão peritoneal multilocular |
| pl | Torbielowaty międzybłoniak otrzewnej | Łagodny wielotorbielowaty międzybłoniak otrzewnej · Torbiel z inkluzjami otrzewnowymi · Wielotorbielowaty międzybłoniak otrzewnej |
| cs | Cystický peritoneální mezoteliom | Benigní multicystický mezoteliom peritonea · Multicystický mezoteliom · Multilokulární inkluzní cysta peritonea |
| uk | Перитоніальна кіста | Доброякісна мультикістозна мезотеліома очеревини · Мультикістозна мезотеліома · Мультилокулярна перитонеальна включена кіста · Циклічна мезотеліома очеревини |
| zh | 腹膜囊性间皮瘤 | 良性多囊性腹膜间皮瘤 |
| tr | Peritoneal kistik mezotelyoma | Multikistik mezotelyoma · Multiloküler peritoneal inklüzyon kisti · Selim multikistik peritoneal mezotelyoma |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | C45.1 | NTBT | attributed | validated |
| ICD-11 | 2F10 | E | specific | validated |
| ICD-11 | XH8U12 | E | specific | validated |
| MONDO | 0006363 | E | validated | |
| MONDO | 6363 | E | validated | |
| UMLS | C1334818 | E | validated | |
| GARD | 10777 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:676030Primary benign peritoneal tumor
rare abdominal surgical diseases; rare neoplastic diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
2 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Cases/families | 150 cases | Worldwide | Case(s) | Validated | [EXPERT] | |
| Point prevalence | Unknown | — | Worldwide | Class only | Validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
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HPO phenotypes
9 annotations · validated 2016-06-01| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0003270 | Abdominal distention | |
| HP:0002027 | Abdominal pain | |
| HP:0002019 | Constipation | |
| HP:0002664 | Neoplasm | |
| HP:0002586 | Peritonitis | |
| Frequent (79-30%) | ||
| HP:0030016 | Dyspareunia | |
| HP:0000132 | Menorrhagia | |
| HP:0100608 | Metrorrhagia | |
| HP:0001824 | Weight loss | |
Run the differential on the 5 obligate / very frequent terms
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/168816
- This record as JSON: /data/d/168816.json