{"orpha":168816,"name":"Peritoneal inclusion cyst","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Benign multicystic peritoneal mesothelioma","Multicystic mesothelioma","Multilocular peritoneal inclusion cyst","Peritoneal cyctic mesothelioma"],"definition":"Peritoneal cystic mesothelioma is a rare benign tumor characterized by the formation of intra-abdominal multilocular cystic masses.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-168816/","orphanet_url":"https://www.orpha.net/en/disease/detail/168816","names":{"fr":{"name":"Kyste d'inclusion péritonéale","synonyms":["Kyste à inclusion péritonéal multiloculaire","Mésothéliome multikystique","Mésothéliome péritonéal multikystique bénin"],"definition":"Le mésothéliome kystique du péritoine est une tumeur bénigne rare caractérisée par la formation de masses kystiques multiloculaires intra-abdominales."},"de":{"name":"Peritoneale Inklusionszyste","synonyms":["Inklusionszyste, multilokuläre peritoneale","Mesotheliom, benignes mulitzystisches peritoneales","Mesotheliom, multizystisches","Peritonealmesotheliom, zystisches"],"definition":"Das Peritoneale zystische Mesotheliom ist ein seltener benigner Tumor und gekennzeichnet durch Bildung einer Vielzahl zystischer Tumormassen im Abdomen."},"es":{"name":"Quiste de inclusión peritoneal","synonyms":["Mesotelioma multiquístico","Mesotelioma peritoneal multiquístico benigno","Mesotelioma peritoneal quístico","Quiste de inclusión peritoneal multilocular"],"definition":"El mesotelioma quístico peritoneal es un tumor benigno poco frecuente caracterizado por la formación de masas quísticas multiloculares intra-abdominales."},"it":{"name":"Cisti da inclusione peritoneale","synonyms":["Cisti peritoneale multioculare da inclusione","Mesotelioma multicistico","Mesotelioma peritoneale multicistico benigno","Mesotelioma cistico peritoneale"],"definition":"Il mesotelioma cistico del peritoneo è un tumore benigno raro, caratterizzato dalla formazione di masse cistiche multiloculari intraddominali."},"nl":{"name":"Peritoneale inclusiecyste","synonyms":["Goedaardig multicystisch peritoneaal mesothelioom","Multicystisch mesothelioom","Multiloculaire peritoneale inclusiecyste","Peritoneaal cystisch mesothelioom"],"definition":"Peritoneaal cystisch mesothelioom is een zeldzame goedaardige tumor, gekenmerkt door de vorming van multiloculaire intra-abdominale cystische massa's."},"pt":{"name":"Quisto de inclusão peritoneal","synonyms":["Mesotelioma multiquístico","Mesotelioma peritoneal multiquistico benigno","Mesotelioma quistico peritoneal","Quisto de inclusão peritoneal multilocular"],"definition":"O mesotelioma peritoneal cístico é um tumor benigno raro caracterizado pela formação de massas císticas multilocular intra-abdominal."},"pl":{"name":"Torbielowaty międzybłoniak otrzewnej","synonyms":["Łagodny wielotorbielowaty międzybłoniak otrzewnej","Torbiel z inkluzjami otrzewnowymi","Wielotorbielowaty międzybłoniak otrzewnej"]},"cs":{"name":"Cystický peritoneální mezoteliom","synonyms":["Benigní multicystický mezoteliom peritonea","Multicystický mezoteliom","Multilokulární inkluzní cysta peritonea"]},"uk":{"name":"Перитоніальна кіста","synonyms":["Доброякісна мультикістозна мезотеліома очеревини","Мультикістозна мезотеліома","Мультилокулярна перитонеальна включена кіста","Циклічна мезотеліома очеревини"],"definition":"Peritoneal cystic mesothelioma is a rare benign tumor characterized by the formation of intra-abdominal multilocular cystic masses."},"zh":{"name":"腹膜囊性间皮瘤","synonyms":["良性多囊性腹膜间皮瘤"],"definition":"腹膜囊性间皮瘤是一种罕见的以腹腔内多发的囊性肿块为特征的良性肿瘤。"},"tr":{"name":"Peritoneal kistik mezotelyoma","synonyms":["Multikistik mezotelyoma","Multiloküler peritoneal inklüzyon kisti","Selim multikistik peritoneal mezotelyoma"]}},"xrefs":[{"source":"ICD-10","code":"C45.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F10","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"358454894"},{"source":"ICD-11","code":"XH8U12","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"168068812"},{"source":"MONDO","code":"0006363","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"6363","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1334818","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"10777","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":676030,"name":"Primary benign peritoneal tumor","classifications":[182,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Unknown"],"onset":["Adult"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":150.0,"area":"Worldwide","status":"Validated","source":"[EXPERT]"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2016-06-01","source":null,"terms":[{"hpo":"HP:0003270","label":"Abdominal distention","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0002027","label":"Abdominal pain","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0002019","label":"Constipation","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0002664","label":"Neoplasm","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0002586","label":"Peritonitis","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0030016","label":"Dyspareunia","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000132","label":"Menorrhagia","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0100608","label":"Metrorrhagia","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0001824","label":"Weight loss","frequency":"Frequent (79-30%)","criteria":null}]}}