raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:158041

Secondary hemophagocytic lymphohistiocytosis

Synonyms: Acquired hemophagocytic lymphohistiocytosis · Reactive hemophagocytic syndrome

Type
Category
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enSecondary hemophagocytic lymphohistiocytosisAcquired hemophagocytic lymphohistiocytosis · Reactive hemophagocytic syndrome
frLymphohistiocytose hémophagocytaire secondaireLymphohistiocytose hémophagocytaire acquis · Syndrome hémophagocytaire réactionnel
deLymphohistiozytose, hämophagozytische, sekundäreHämophagozytisches Syndrom, reaktives · Lymphohistiozytose, hämophagozytische, erworbene
esLinfohistiocitosis hemofagocítica secundariaLinfohistiocitosis hemofagocítica adquirida · Síndrome hemofagocítico reactivo
itLinfoistiocitosi emofagocitica secondariaLinfoistiocitosi emofagocitica acquisita · Sindrome emofagocitica reattiva
nlSecundaire hemofagocytaire lymfohistiocytoseReactief hemofagocytair syndroom · Verworven hemofagocytaire lymfohistiocytose
ptLinfo-histiocitose hemofagocítica secundária
plWtórna limfohistiocytoza hemofagocytarnaNabyta limfohistiocytoza hemofagocytarna · Reaktywny zespół hemofagocytarny
csSekundární hemofagocytující lymfohistiocytózaZískaná hemofagocytující lymfohistiocytóza · Reaktivní hemofagocytický syndrom
ukВторинний гемофагоцитарний лімфогістіоцитозНабутий гемофагоцитарний лімфогістіоцитоз · Реактивний гемофагоцитарний синдром
zh继发性噬血细胞性淋巴组织细胞增多症获得性噬血细胞性淋巴组织细胞增多症
trSekonder hemofagositik lenfohistiyositozReaktif hemofagositik sendrom · Edinsel hemofagositik lenfohistiyositoz
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-113B62.YNTBTindexvalidated
MONDO0015542Evalidated
MONDO15542Evalidated
UMLSC0019068Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (3):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card