{"orpha":158041,"name":"Secondary hemophagocytic lymphohistiocytosis","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Acquired hemophagocytic lymphohistiocytosis","Reactive hemophagocytic syndrome"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-158041/","orphanet_url":"https://www.orpha.net/en/disease/detail/158041","names":{"fr":{"name":"Lymphohistiocytose hémophagocytaire secondaire","synonyms":["Lymphohistiocytose hémophagocytaire acquis","Syndrome hémophagocytaire réactionnel"]},"de":{"name":"Lymphohistiozytose, hämophagozytische, sekundäre","synonyms":["Hämophagozytisches Syndrom, reaktives","Lymphohistiozytose, hämophagozytische, erworbene"]},"es":{"name":"Linfohistiocitosis hemofagocítica secundaria","synonyms":["Linfohistiocitosis hemofagocítica adquirida","Síndrome hemofagocítico reactivo"]},"it":{"name":"Linfoistiocitosi emofagocitica secondaria","synonyms":["Linfoistiocitosi emofagocitica acquisita","Sindrome emofagocitica reattiva"]},"nl":{"name":"Secundaire hemofagocytaire lymfohistiocytose","synonyms":["Reactief hemofagocytair syndroom","Verworven hemofagocytaire lymfohistiocytose"]},"pt":{"name":"Linfo-histiocitose hemofagocítica secundária"},"pl":{"name":"Wtórna limfohistiocytoza hemofagocytarna","synonyms":["Nabyta limfohistiocytoza hemofagocytarna","Reaktywny zespół hemofagocytarny"]},"cs":{"name":"Sekundární hemofagocytující lymfohistiocytóza","synonyms":["Získaná hemofagocytující lymfohistiocytóza","Reaktivní hemofagocytický syndrom"]},"uk":{"name":"Вторинний гемофагоцитарний лімфогістіоцитоз","synonyms":["Набутий гемофагоцитарний лімфогістіоцитоз","Реактивний гемофагоцитарний синдром"]},"zh":{"name":"继发性噬血细胞性淋巴组织细胞增多症","synonyms":["获得性噬血细胞性淋巴组织细胞增多症"]},"tr":{"name":"Sekonder hemofagositik lenfohistiyositoz","synonyms":["Reaktif hemofagositik sendrom","Edinsel hemofagositik lenfohistiyositoz"]}},"xrefs":[{"source":"ICD-11","code":"3B62.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"239985204"},{"source":"MONDO","code":"0015542","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"15542","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0019068","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98004,"name":"Rare immune disease"},"parents":[{"orpha":158032,"name":"Hemophagocytic syndrome","classifications":[195]}],"children":[{"orpha":158057,"name":"Acquired hemophagocytic lymphohistiocytosis associated with malignant disease","type":"Particular clinical situation in a disease or syndrome"},{"orpha":158048,"name":"Hemophagocytic syndrome associated with an infection","type":"Particular clinical situation in a disease or syndrome"},{"orpha":158061,"name":"Macrophage activation syndrome","type":"Clinical syndrome"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}