Klüver-Bucy syndrome
- Type
- Clinical syndrome
- Group
- Disorder
- Status
- active
A rare neurologic disease characterized by visual agnosia, hyperorality (strong tendency to examine objects orally), hypermetamorphosis (described as the irresistible impulse to notice and react to everything within sight), hypersexuality, changes in dietary habits and hyperphagia, placidity, and amnesia, due to bilateral lesions of the temporal lobe including the hippocampus and amygdala.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Klüver-Bucy syndrome | |
| fr | Syndrome de Klüver-Bucy | |
| de | Klüver-Bucy-Syndrom | |
| es | Síndrome de Klüver-Bucy | |
| it | Sindrome di Klüver-Bucy | |
| nl | Syndroom van Klüver-Bucy | |
| pt | Síndrome de Klüver-Bucy | |
| pl | Zespół Klüvera i Bucy'ego | |
| cs | Klüverův-Bucyho syndrom | Klüver-Bucyho syndrom |
| uk | Синдром Клювера-Бюсі | |
| zh | Kl³ver-Bucy 综合征 | |
| tr | Klüver-Bucy sendromu |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | G04.8 | NTBT | attributed | validated |
| MONDO | 0005817 | E | validated | |
| MeSH | D020232 | E | validated | |
| UMLS | C0270707 | E | validated | |
| GARD | 6840 | E | validated | |
| MedDRA | 10066431 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98033Rare neurologic disease with psychiatric involvement
rare neurological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
0 recordsNo prevalence record in this release.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/157823
- This record as JSON: /data/d/157823.json