raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:156143

Predominantly medium-vessel vasculitis

Type
Clinical group
Group
Group of disorders
Status
active

This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPredominantly medium-vessel vasculitis
frVascularite des vaisseaux de moyen calibre
deVaskulitis mittelgroßer Gefäße
esVasculitis de vasos medios predominantemente
itVasculite con interessamento prevalente dei vasi medi
nlVasculitis van overwegend middelgrote bloedvaten
ptVasculite predominantemente dos vasos médios
plDominujące zapalenie średnich naczyń
csVaskulitida převážně středních cév
ukСистемний васкуліт з переважним ураженням судин середнього діаметра
zh主要累及中等血管的血管炎
trAğırlıklı orta-damar vasküliti
2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
MONDO15489Evalidated
UMLSC5680654Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

Children (6):

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card