{"orpha":156143,"name":"Predominantly medium-vessel vasculitis","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-156143/","orphanet_url":"https://www.orpha.net/en/disease/detail/156143","names":{"fr":{"name":"Vascularite des vaisseaux de moyen calibre"},"de":{"name":"Vaskulitis mittelgroßer Gefäße"},"es":{"name":"Vasculitis de vasos medios predominantemente"},"it":{"name":"Vasculite con interessamento prevalente dei vasi medi"},"nl":{"name":"Vasculitis van overwegend middelgrote bloedvaten"},"pt":{"name":"Vasculite predominantemente dos vasos médios"},"pl":{"name":"Dominujące zapalenie średnich naczyń"},"cs":{"name":"Vaskulitida převážně středních cév"},"uk":{"name":"Системний васкуліт з переважним ураженням судин середнього діаметра"},"zh":{"name":"主要累及中等血管的血管炎"},"tr":{"name":"Ağırlıklı orta-damar vasküliti"}},"xrefs":[{"source":"MONDO","code":"15489","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680654","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":52759,"name":"Vasculitis","classifications":[196,198]}],"children":[{"orpha":36258,"name":"Buerger disease","type":"Disease"},{"orpha":404553,"name":"Deficiency of adenosine deaminase 2","type":"Disease"},{"orpha":2331,"name":"Kawasaki disease","type":"Disease"},{"orpha":767,"name":"Polyarteritis nodosa","type":"Disease"},{"orpha":140989,"name":"Primary angiitis of the central nervous system","type":"Disease"},{"orpha":596753,"name":"VEXAS syndrome","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}