Lemierre syndrome
Synonyms: Lemierre postanginal sepsis · Postanginal sepsis secondary to orophyngeal infection · Septic phlebitis of the internal jugular vein
- Type
- Disease
- Group
- Disorder
- Age of onset
- Adolescent
- Status
- active
Lemierre syndrome is a rare, potentially lethal, oropharyngeal infectious disease occurring in immunocompetent adolescents and young adults that is mainly due to <i>Fusobacterium necrophorum</i> and that is characterized by septic thrombophlebitis of the internal jugular vein that leads to septic, usually pulmonary, embolism, associated with ENT (ear, nose, and throat) infection that manifests with fever, neck pain, and tonsillopharyngitis.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Lemierre syndrome | Lemierre postanginal sepsis · Postanginal sepsis secondary to orophyngeal infection · Septic phlebitis of the internal jugular vein |
| fr | Syndrome de Lemierre | Sepsis post-angine de Lemierre · Sepsis post-angine secondaire à une infection oropharyngée · Thrombophlébite septique de la veine jugulaire interne |
| de | Lemierre-Syndrom | Postangina-Sepsis Lemierre · Postanginale Sepsis nach oropharyngealer Infektion · Septische Phlebitis der internen Jugularvene |
| es | Síndrome de Lemierre | Flebitis séptica de la vena yugular interna · Sepsis postangina secundaria a infección orofaríngea · Sepsis postanginal de Lemierre · Sepsis postanginal secundaria a una infección orofaríngea |
| it | Sindrome di Lemierre | Flebite settica della vena giugulare interna · Sepsi post-angina di Lemierre · Sepsi post-angina secondaria a infezioni orofaringee |
| nl | Lemierresyndroom | Postanginale sepsis secundair aan orofaryngeale infectie · Postanginale sepsis van Lemierre · Septische flebitis van de inwendige halsader |
| pt | Síndrome de Lemierre | |
| pl | Zespół Lemierre'a | Poanginowa posocznica Lemierre'a · Septyczne zapalenie żyły szyjnej wewnętrznej · Wtórna posocznica poanginowa po infekcji gardła |
| cs | Lemierrův syndrom | Lemierrova postanginózní sepse · Sekundární postanginózní sepse po orofaryngeální infekci · Septická flebitida vnitřní krční žíly |
| uk | Синдром Лемєра | Постангінальний сепсис Лемєра · Постангінальний сепсис, спричинений інфекцією ротоглотки · Септичний флебіт внутрішньої яремної вени |
| zh | Lemierre综合征 | 口咽部感染所致咽峡后脓毒血症 |
| tr | Lemierre sendromu | Lemierre postanginal sepsis · İç juguler venin septik flebiti · Orofingeal enfeksiyona sekonder postanginal sepsis |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | I80.8 | NTBT | attributed | validated |
| ICD-11 | 1C4Y | NTBT | attributed | validated |
| MONDO | 0015306 | E | validated | |
| MeSH | D057831 | E | validated | |
| UMLS | C0343525 | E | validated | |
| GARD | 6882 | E | validated | |
| MedDRA | 10065552 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:163582Rare bacterial infectious disease
rare infectious diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
3 records| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Annual incidence | 1-5 / 10 000 | 10 / 100 000 | Europe | Value and class | Not yet validated | 20181152[PMID] |
| Annual incidence | 1-5 / 10 000 | 36 / 100 000 | Denmark | Value and class | Validated | 22633566[PMID] |
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/137839
- This record as JSON: /data/d/137839.json