Arachnoiditis
Synonyms: Adhesive arachnoiditis · Chronic arachnoiditis
- Type
- Disease
- Group
- Disorder
- Inheritance
- Not applicable
- Age of onset
- All ages
- Status
- active
A chronic inflammation of the arachnoid layer of the meninges, of which adhesive arachnoiditis is the most severe form, characterized by debilitating, intractable neurogenic back and limb pain and a range of other neurological problems.
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Arachnoiditis | Adhesive arachnoiditis · Chronic arachnoiditis |
| fr | Arachnoïdite | Arachnoïdite adhésive · Arachnoïdite chronique |
| de | Arachnoiditis | Arachnoiditis, adhäsive · Arachnoiditis, chronische |
| es | Aracnoiditis | Aracnoiditis adhesiva · Aracnoiditis crónica |
| it | Aracnoidite | Aracnoidite adesiva · Aracnoidite cronica |
| nl | Arachnoïditis | Adhesieve arachnoïditis · Chronische arachnoïditis |
| pt | Aracnoidite adesiva | |
| pl | Zapalenie pajęczynówki | Przewlekłe zapalenie pajęczynówki · Zlepne zapalenie pajęczynówki |
| cs | Arachnoiditida | Adhezivní arachnoiditida · Chronická arachnoiditida |
| uk | Арахноїдит | Адгезивний арахноїдит · Хронічний арахноїдит |
| zh | 蛛网膜炎 | 粘连性蛛网膜炎 |
| tr | Araknoidit | Kronik araknoidit · Adezyon araknoidit |
Definition in:
Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| OMIM | 182950 | BTNT | validated | |
| ICD-10 | G03.9 | NTBT | attributed | validated |
| ICD-11 | 8E40.3 | E | specific | validated |
| MONDO | 0015304 | E | validated | |
| MeSH | D001100 | E | validated | |
| UMLS | C0003708 | E | validated | |
| GARD | 5839 | E | validated | |
| MedDRA | 10003074 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:98006Rare neurologic disease
rare neurological diseases
No children.
Genes
0 directOrphanet records no gene directly on this code.
Prevalence and incidence
1 record| Type | Class | Value | Area | Qualification | Validation | Source |
|---|---|---|---|---|---|---|
| Point prevalence | Unknown | — | Worldwide | Class only | Not yet validated | ORPHANET |
Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.
HPO phenotypes
15 annotations · validated 2016-06-01| HPO | Term (as annotated by Orphanet) | Diagnostic |
|---|---|---|
| Very frequent (99-80%) | ||
| HP:0000478 | Abnormality of the eye | |
| HP:0000504 | Abnormality of vision | |
| HP:0002829 | Arthralgia | |
| HP:0000365 | Hearing impairment | |
| HP:0001265 | Hyporeflexia | |
| HP:0001287 | Meningitis | |
| HP:0001324 | Muscle weakness | |
| HP:0003401 | Paresthesia | |
| HP:0000763 | Sensory neuropathy | |
| HP:0000360 | Tinnitus | |
| Frequent (79-30%) | ||
| HP:0000970 | Anhidrosis | |
| Occasional (29-5%) | ||
| HP:0012378 | Fatigue | |
| HP:0000238 | Hydrocephalus | |
| HP:0002076 | Migraine | |
| HP:0002839 | Urinary bladder sphincter dysfunction | |
Run the differential on the 10 obligate / very frequent terms
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/137817
- This record as JSON: /data/d/137817.json