raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:129

Pseudopelade of Brocq

Type
Disease
Group
Disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

Pseudo-pelade of Brocq is a rare hair abnormality characterized by onset in adulthood of soft, irregular, flesh-toned patches of alopecia primarily in the parietal and vertex portions of the scalp, without follicular hyperkeratosis or perifollicular inflammation.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enPseudopelade of Brocq
frPseudo-pelade de Brocq
dePseudopelade Brocq
esPseudopelada de Brocq
itPseudoalopecia areata di Brocq
nlPseudopelade van Brocq
ptPseudo-pelada de Brocq
plŁysienie rzekomo bliznowaciejące Brocqa
csAlopecia areata atrophicansPseudopelade Brocq
ukПсевдопелада Брока
zhBrocq假性斑秃
trBrocq psödopelad

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10L66.0NTBTattributedvalidated
ICD-11ED70.5YNTBTindexvalidated
MONDO0015261Evalidated
UMLSC0086873Evalidated
GARD4536Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyNot yet validatedORPHANET

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

7 annotations · validated 2026-02-24
HPOTerm (as annotated by Orphanet)Diagnostic
Very frequent (99-80%)
HP:0001595Abnormality of the hair
HP:0001596Alopecia
HP:0004529Atrophic, patchy alopecia
HP:0002287Progressive alopecia
Frequent (79-30%)
HP:0001053Hypopigmented skin patches
Excluded (0%)
HP:0002960Autoimmunity
HP:0025084Folliculitis

Run the differential on the 4 obligate / very frequent terms

Annotation source: 40109647[PMID]_37196297[PMID]_25114452[PMID]

7

Sources for this card