raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:1235

OBSOLETE: Ectodermal dysplasia-absent dermatoglyphs syndrome

inactive · referred to ORPHA:1658Absence of fingerprints-congenital milia syndrome

Synonyms: OBSOLETE: Basan syndrome

Type
Disease
Group
Disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Absence of fingerprints-congenital milia syndrome

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Ectodermal dysplasia-absent dermatoglyphs syndromeOBSOLETE: Basan syndrome
frOBSOLETE : Syndrome de BasanOBSOLETE : Syndrome de dysplasie ectodermique-dermatoglyphes absents
deOBSOLET: Basan-SyndromOBSOLET: Ektodermale Dysplasie mit fehlenden Dermatoglyphen
esOBSOLETO: Síndrome de displasia ectodérmica-dermatoglifos ausentesOBSOLETO: Síndrome de Basan
itOBSOLETO: Sindrome displasia ectodermica-assenza dei dermatoglifiOBSOLETO: Sindrome di Basan
nlOBSOLEET: Ectodermale dysplasie - afwezige dermatoglyfen-syndroomOBSOLEET: Syndroom van Basan
ptOBSOLETO: Síndrome de displasia ectodérmica-dermatóglifos ausentes
plNIEAKTUALNE: Dysplazja ektodermalna - brak dermatoglifówNIEAKTUALNE: Zespół Basana
csNEAKTUÁLNÍ: Syndrom zahrnující ektodermální dysplázii a absenci dermatoglyfůNEAKTUÁLNÍ: Basanův syndrom
ukЗАСТАРІЛО: Синдром ектодермальної дисплазії з відсутністю дерматогліфівЗАСТАРІЛО: Синдром Басана
zh弃用:真皮发育不良-皮纹缺乏综合征Basan综合征
trEski adı: Ektodermal displazi olmayan dermatoglif sendromuBasan sendromu
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card