raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:1160

Chylous ascites

Type
Disease
Group
Disorder
Age of onset
All ages
Status
active

Chylous ascites is a rare form of ascites caused by accumulation of lymph in the peritoneal cavity, usually due to intra-abdominal malignancy, liver cirrhosis or abdominal surgery complications, and present with painless but progressive abdominal distension, dyspnea and weight gain.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enChylous ascites
frAscite chyleuse
deAszites, chylöserChylaszites
esAscitis quilosa
itAscite chilosa
nlChyleuze ascites
ptAscite quilosa
plWodobrzusze mleczowe
csChylózní ascites
ukХілозний асцит
zh乳糜腹水
trŞilöz asit

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
OMIM208300Evalidated
ICD-10I89.8NTBTindexvalidated
ICD-11DC51.0Especificvalidated
MONDO0008829Evalidated
MeSHD002915Evalidated
UMLSC0008732Evalidated
GARD1359Evalidated
MedDRA10003446Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

1 record
TypeClassValueAreaQualificationValidationSource
Point prevalenceUnknown—WorldwideClass onlyValidatedORPHANET_22319743[PMID]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

6

HPO phenotypes

7 annotations · validated 2016-06-01
HPOTerm (as annotated by Orphanet)Diagnostic
Very frequent (99-80%)
HP:0001541Ascites
HP:0001004Lymphedema
Frequent (79-30%)
HP:0001482Subcutaneous nodule
Occasional (29-5%)
HP:0002242Abnormal intestine morphology
HP:0000501Glaucoma
HP:0002664Neoplasm
HP:0001733Pancreatitis

Run the differential on the 2 obligate / very frequent terms

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Sources for this card