{"orpha":1160,"name":"Chylous ascites","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Chylous ascites is a rare form of ascites caused by accumulation of lymph in the peritoneal cavity, usually due to intra-abdominal malignancy, liver cirrhosis or abdominal surgery complications, and present with painless but progressive abdominal distension, dyspnea and weight gain.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-1160/","orphanet_url":"https://www.orpha.net/en/disease/detail/1160","names":{"fr":{"name":"Ascite chyleuse","definition":"L'ascite chyleuse est une forme rare d'ascite causée par l'accumulation de lymphe dans la cavité péritonéale, généralement secondaire à un cancer intra-abdominal, à une cirrhose hépatique ou à une chirurgie abdominale. Elle se manifeste par une distension abdominale indolore mais progressive, une dyspnée et une prise de poids."},"de":{"name":"Aszites, chylöser","synonyms":["Chylaszites"],"definition":"Chylaszites, eine seltene Aszitesform, ist verursacht durch Ansammlung von Lymphe in der Bauchhöhle, meist bei bösartigem intra-abdominellem Tumor oder Leberzirrhose oder als Komplikation eines chirurgischen Eingriffes in der Bauchhöhle. Symptome sind nicht schmerzhafte aber progrediente Auftreibung des Abdomens, Dyspnoe und Gewichtszunahme."},"es":{"name":"Ascitis quilosa","definition":"La ascitis quilosa es una forma poco frecuente de ascitis causada por la acumulación de linfa en la cavidad peritoneal, normalmente debida a un tumor intra-abdominal, una cirrosis hepática o complicaciones tras la cirugía abdominal, y se presenta sin dolor pero con distensión abdominal progresiva, disnea y aumento de peso."},"it":{"name":"Ascite chilosa","definition":"L'ascite chilosa è una forma rara di ascite, causata dall'accumulo di linfa nella cavità peritoneale; di solito è causata da un tumore maligno dell'addome, cirrosi epatica o complicazioni secondarie alla chirurgia dell'addome. Si manifesta con distensione addominale progressiva indolore, dispnea e aumento del peso."},"nl":{"name":"Chyleuze ascites","definition":"Een zeldzame vorm van ascites, veroorzaakt door accumulatie van lymfe in peritoneale holte, meestal ten gevolge van intra-abdominale maligniteit, levercirrose of complicaties van chirurgie van abdomen, en zich presenterend met pijnloze maar progressieve abdominale distensie, dyspneu en gewichtstoename."},"pt":{"name":"Ascite quilosa"},"pl":{"name":"Wodobrzusze mleczowe"},"cs":{"name":"Chylózní ascites"},"uk":{"name":"Хілозний асцит","definition":"Chylous ascites is a rare form of ascites caused by accumulation of lymph in the peritoneal cavity, usually due to intra-abdominal malignancy, liver cirrhosis or abdominal surgery complications, and present with painless but progressive abdominal distension, dyspnea and weight gain."},"zh":{"name":"乳糜腹水"},"tr":{"name":"Şilöz asit"}},"xrefs":[{"source":"OMIM","code":"208300","qualifier":"E","icd_relation":null,"validated":true},{"source":"ICD-10","code":"I89.8","qualifier":"NTBT","icd_relation":"index","validated":true},{"source":"ICD-11","code":"DC51.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"768846885"},{"source":"MONDO","code":"0008829","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D002915","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0008732","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"1359","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10003446","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":165711,"name":"Rare abdominal surgical disease"},"parents":[{"orpha":165711,"name":"Rare abdominal surgical disease","classifications":[182]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET_22319743[PMID]"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2016-06-01","source":null,"terms":[{"hpo":"HP:0001541","label":"Ascites","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0001004","label":"Lymphedema","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0001482","label":"Subcutaneous nodule","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0002242","label":"Abnormal intestine morphology","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000501","label":"Glaucoma","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002664","label":"Neoplasm","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0001733","label":"Pancreatitis","frequency":"Occasional (29-5%)","criteria":null}]}}