ORPHA:1137
OBSOLETE: Pulmonary aortic stenosis obstructive uropathy
inactive · referred to ORPHA:102285Multiple congenital anomalies/dysmorphic syndrome without intellectual disability
Synonyms: OBSOLETE: Kashani-Strom-Utley syndrome
- Type
- Disease
- Group
- Disorder
- Status
- inactive
- Flag
- Obsolete entity
This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Multiple congenital anomalies/dysmorphic syndrome without intellectual disability
1
Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | OBSOLETE: Pulmonary aortic stenosis obstructive uropathy | OBSOLETE: Kashani-Strom-Utley syndrome |
| fr | OBSOLETE : Syndrome d'artre pulmonaire et aorte hypoplasiques-uropathie obstructive | OBSOLETE : Syndrome de Kashani-Strom-Utley |
| de | OBSOLET: Pulmonalarterienstenose mit obstruktiver Uropathie | OBSOLET: Kashani-Strom-Utley-Syndrom |
| es | OBSOLETO: Uropatía obstructiva por estenosis aórtica pulmonar | OBSOLETO: Síndrome de Kashani-Strom-Utley |
| it | OBSOLETO: stenosi aortica polmonare - uropatia ostruttiva | OBSOLETO: Sindrome di Kashani-Strom-Utley |
| nl | OBSOLEET: Longslagaderstenose obstructieve uropathie | OBSOLEET: Kashani-Strom-Utleysyndroom |
| pt | OBSOLETO: Estenose aortica pulmonar-uropatia obstrutiva | |
| pl | NIEAKTUALNE: Zwezenie tetnicy plucnej - uropatia zaporowa | NIEAKTUALNE: Zespół Kashani, Stroma i Utley'a |
| cs | NEAKTUÁLNÍ: Obstrukční uropatie při stenóze plicní aorty | = en |
| uk | ЗАСТАРІЛО: Обструктивна уропатія з легеневим аортальним стенозом | Синдром Кашані-Строма-Утлі |
| zh | 弃用:肺动脉狭窄合并梗阻性尿路病 | Kashani-Strom-Utley综合征 |
| tr | Eski adı: Pulmoner aort darlığı obstrüktif üropati | Kashani-Strom-Utley sendromu |
2
Cross-references
qualifier = Orphanet mapping relationNo cross-references in this release.
3
Classification
Not placed in any Orphanet classification in this release.
No children.
4
Genes
0 directOrphanet records no gene directly on this code.
5
Prevalence and incidence
0 recordsNo prevalence record in this release.
6
HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
7
Sources for this card
- Orphanet page: orpha.net/en/disease/detail/1137
- This record as JSON: /data/d/1137.json