raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:1137

OBSOLETE: Pulmonary aortic stenosis obstructive uropathy

inactive · referred to ORPHA:102285Multiple congenital anomalies/dysmorphic syndrome without intellectual disability

Synonyms: OBSOLETE: Kashani-Strom-Utley syndrome

Type
Disease
Group
Disorder
Status
inactive
Flag
Obsolete entity

This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Multiple congenital anomalies/dysmorphic syndrome without intellectual disability

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enOBSOLETE: Pulmonary aortic stenosis obstructive uropathyOBSOLETE: Kashani-Strom-Utley syndrome
frOBSOLETE : Syndrome d'artre pulmonaire et aorte hypoplasiques-uropathie obstructiveOBSOLETE : Syndrome de Kashani-Strom-Utley
deOBSOLET: Pulmonalarterienstenose mit obstruktiver UropathieOBSOLET: Kashani-Strom-Utley-Syndrom
esOBSOLETO: Uropatía obstructiva por estenosis aórtica pulmonarOBSOLETO: Síndrome de Kashani-Strom-Utley
itOBSOLETO: stenosi aortica polmonare - uropatia ostruttivaOBSOLETO: Sindrome di Kashani-Strom-Utley
nlOBSOLEET: Longslagaderstenose obstructieve uropathieOBSOLEET: Kashani-Strom-Utleysyndroom
ptOBSOLETO: Estenose aortica pulmonar-uropatia obstrutiva
plNIEAKTUALNE: Zwezenie tetnicy plucnej - uropatia zaporowaNIEAKTUALNE: Zespół Kashani, Stroma i Utley'a
csNEAKTUÁLNÍ: Obstrukční uropatie při stenóze plicní aorty= en
ukЗАСТАРІЛО: Обструктивна уропатія з легеневим аортальним стенозомСиндром Кашані-Строма-Утлі
zh弃用:肺动脉狭窄合并梗阻性尿路病Kashani-Strom-Utley综合征
trEski adı: Pulmoner aort darlığı obstrüktif üropatiKashani-Strom-Utley sendromu
2

Cross-references

qualifier = Orphanet mapping relation

No cross-references in this release.

3

Classification

Not placed in any Orphanet classification in this release.

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card