{"orpha":1137,"name":"OBSOLETE: Pulmonary aortic stenosis obstructive uropathy","type":"Disease","group":"Disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":["OBSOLETE: Kashani-Strom-Utley syndrome"],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Multiple congenital anomalies/dysmorphic syndrome without intellectual disability","url":"https://raremap.alftech.space/d/ORPHA-1137/","orphanet_url":"https://www.orpha.net/en/disease/detail/1137","names":{"fr":{"name":"OBSOLETE : Syndrome d'artre pulmonaire et aorte hypoplasiques-uropathie obstructive","synonyms":["OBSOLETE : Syndrome de Kashani-Strom-Utley"]},"de":{"name":"OBSOLET: Pulmonalarterienstenose mit obstruktiver Uropathie","synonyms":["OBSOLET: Kashani-Strom-Utley-Syndrom"]},"es":{"name":"OBSOLETO: Uropatía obstructiva por estenosis aórtica pulmonar","synonyms":["OBSOLETO: Síndrome de Kashani-Strom-Utley"]},"it":{"name":"OBSOLETO: stenosi aortica polmonare - uropatia ostruttiva","synonyms":["OBSOLETO: Sindrome di Kashani-Strom-Utley"]},"nl":{"name":"OBSOLEET: Longslagaderstenose obstructieve uropathie","synonyms":["OBSOLEET: Kashani-Strom-Utleysyndroom"]},"pt":{"name":"OBSOLETO: Estenose aortica pulmonar-uropatia obstrutiva"},"pl":{"name":"NIEAKTUALNE: Zwezenie tetnicy plucnej - uropatia zaporowa","synonyms":["NIEAKTUALNE: Zespół Kashani, Stroma i Utley'a"]},"cs":{"name":"NEAKTUÁLNÍ: Obstrukční uropatie při stenóze plicní aorty","synonyms":["OBSOLETE: Kashani-Strom-Utley syndrome"]},"uk":{"name":"ЗАСТАРІЛО: Обструктивна уропатія з легеневим аортальним стенозом","synonyms":["Синдром Кашані-Строма-Утлі"]},"zh":{"name":"弃用：肺动脉狭窄合并梗阻性尿路病","synonyms":["Kashani-Strom-Utley综合征"]},"tr":{"name":"Eski adı: Pulmoner aort darlığı obstrüktif üropati","synonyms":["Kashani-Strom-Utley sendromu"]}},"xrefs":[],"associations":[{"type":"Referred to","orpha":102285,"name":"Multiple congenital anomalies/dysmorphic syndrome without intellectual disability"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}