ORPHA:100056
Acquired angioedema type 1
Synonyms: Acquired angioneurotic edema type 1
- Type
- Clinical subtype
- Group
- Subtype of disorder
- Inheritance
- Not applicable
- Age of onset
- Adult
- Status
- active
A type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway.
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Names in Orphadata languages
12 of 12 languages| Lang | Name | Synonyms |
|---|---|---|
| en | Acquired angioedema type 1 | Acquired angioneurotic edema type 1 |
| fr | Angio-oedème acquis type I | Angio-oedème bradykinique acquis type I · Oedème angioneurotique acquis type I |
| de | Angioödem, erworbenes, Typ 1 | |
| es | Angioedema adquirido tipo 1 | AEA 1 |
| it | Angioedema acquisito, tipo 1 | Edema angioneurotico acquisito, tipo 1 |
| nl | Verworven angio-oedeem type 1 | Verworven angioneurotisch oedeem type 1 |
| pt | Angioedema adquirido, tipo I | |
| pl | Nabyty obrzęk naczynioruchowy typu 1 | Nabyty obrzęk angioneurotyczny typu 1 |
| cs | Získaný angioedém, typ 1 | Získaný angioneurotický edém, typ 1 |
| uk | Набутий ангіоневротичний набряк, тип 1 | Набутий ангіоневротичний набряк типу 1 |
| zh | 获得性血管性水肿1型 | 获得性血管神经性水肿1型 |
| tr | Edinsel anjiyoödem tip 1 | Edinsel anjiyonörotik ödem tip 1 |
Definition in:
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Cross-references
qualifier = Orphanet mapping relation| Source | Code | Qualifier | ICD relation | Validation |
|---|---|---|---|---|
| ICD-10 | T78.3 | NTBT | attributed | validated |
| ICD-11 | 4A00.15 | NTBT | index | validated |
| MONDO | 0015056 | E | validated | |
| UMLS | C5680380 | E | validated |
E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.
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Classification
Preferential parent (Orphanet linearisation):
Parents in the classifications (1):
- ORPHA:528663Acquired angioedema with C1Inh deficiency
rare immunological diseases
No children.
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Genes
0 directOrphanet records no gene directly on this code.
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Prevalence and incidence
0 recordsNo prevalence record in this release.
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HPO phenotypes
Orphanet has no HPO annotation for this code in this release.
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Sources for this card
- Orphanet page: orpha.net/en/disease/detail/100056
- This record as JSON: /data/d/100056.json