raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:100056

Acquired angioedema type 1

Synonyms: Acquired angioneurotic edema type 1

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

A type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAcquired angioedema type 1Acquired angioneurotic edema type 1
frAngio-oedème acquis type IAngio-oedème bradykinique acquis type I · Oedème angioneurotique acquis type I
deAngioödem, erworbenes, Typ 1
esAngioedema adquirido tipo 1AEA 1
itAngioedema acquisito, tipo 1Edema angioneurotico acquisito, tipo 1
nlVerworven angio-oedeem type 1Verworven angioneurotisch oedeem type 1
ptAngioedema adquirido, tipo I
plNabyty obrzęk naczynioruchowy typu 1Nabyty obrzęk angioneurotyczny typu 1
csZískaný angioedém, typ 1Získaný angioneurotický edém, typ 1
ukНабутий ангіоневротичний набряк, тип 1Набутий ангіоневротичний набряк типу 1
zh获得性血管性水肿1型获得性血管神经性水肿1型
trEdinsel anjiyoödem tip 1Edinsel anjiyonörotik ödem tip 1

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10T78.3NTBTattributedvalidated
ICD-114A00.15NTBTindexvalidated
MONDO0015056Evalidated
UMLSC5680380Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card