{"orpha":100056,"name":"Acquired angioedema type 1","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Acquired angioneurotic edema type 1"],"definition":"A type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-100056/","orphanet_url":"https://www.orpha.net/en/disease/detail/100056","names":{"fr":{"name":"Angio-oedème acquis type I","synonyms":["Angio-oedème bradykinique acquis type I","Oedème angioneurotique acquis type I"],"definition":"L'angioedème acquis de type 1 est une forme d'angioedème d'angioedème acquis (AOA) caractérisée par un oedème aigu des tissus sous-cutanés et sous-muqueux des viscères et/ou des voies aériennes supérieures."},"de":{"name":"Angioödem, erworbenes, Typ 1","definition":"Das Erworbene Angioödem Typ 1 (AAE1), eine Form des Erworbenen Angioödems (AAE; s. dort), ist gekennzeichnet durch akutes Ödem in subkutanen Geweben, inneren Organen und/oder oberen Atemwegen."},"es":{"name":"Angioedema adquirido tipo 1","synonyms":["AEA 1"],"definition":"Es un tipo de angioedema adquirido (AEA) caracterizado por un edema agudo en los tejidos subcutáneos, las vísceras y/o las vías aéreas superiores."},"it":{"name":"Angioedema acquisito, tipo 1","synonyms":["Edema angioneurotico acquisito, tipo 1"],"definition":"L'angioedema acquisito tipo 1 (AAE 1) è una forma di angioedema acquisito (si veda questo termine), caratterizzata da edema acuto nel sottocutaneo, nei visceri e/o nelle vie respiratorie superiori."},"nl":{"name":"Verworven angio-oedeem type 1","synonyms":["Verworven angioneurotisch oedeem type 1"],"definition":"Een type van verworven angio-oedeem, gekarakteriseerd door acuut oedeem in onderhuidse weefsels, ingewanden en/of de bovenste luchtwegen."},"pt":{"name":"Angioedema adquirido, tipo I"},"pl":{"name":"Nabyty obrzęk naczynioruchowy typu 1","synonyms":["Nabyty obrzęk angioneurotyczny typu 1"]},"cs":{"name":"Získaný angioedém, typ 1","synonyms":["Získaný angioneurotický edém, typ 1"]},"uk":{"name":"Набутий ангіоневротичний набряк, тип 1","synonyms":["Набутий ангіоневротичний набряк типу 1"],"definition":"A type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway."},"zh":{"name":"获得性血管性水肿1型","synonyms":["获得性血管神经性水肿1型"]},"tr":{"name":"Edinsel anjiyoödem tip 1","synonyms":["Edinsel anjiyonörotik ödem tip 1"]}},"xrefs":[{"source":"ICD-10","code":"T78.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4A00.15","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"850631759"},{"source":"MONDO","code":"0015056","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680380","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":528663,"name":"Acquired angioedema with C1Inh deficiency","classifications":[195]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[],"phenotypes":null}