raremaprare-disease reference indexOrphadata 2026-06-23 · HPO 2026-09-01
ORPHA:100055

Acquired angioedema type 2

Synonyms: AAE 2 · AAE II · Acquired angioneurotic edema type 2

Type
Clinical subtype
Group
Subtype of disorder
Inheritance
Not applicable
Age of onset
Adult
Status
active

A type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway.

1

Names in Orphadata languages

12 of 12 languages
LangNameSynonyms
enAcquired angioedema type 2AAE 2 · AAE II · Acquired angioneurotic edema type 2
frAngio-oedème acquis type IIAAE 2 · AAE II · Angio-oedème bradykinique acquis type II · Oedème angioneurotique acquis type II
deAngioödem, erworbenes, Typ 2
esAngioedema adquirido tipo 2Edema angioneurótico adquirido tipo 2 · AAE II · AEA 2
itAngioedema acquisito, tipo 2AAE 2 · AAE II · Edema angioneurotico acquisito, tipo 2
nlVerworven angio-oedeem type 2AAE 2 · AAE II · Verworven angioneurotisch oedeem type 2
ptAngioedema adquirido, tipo II
plNabyty obrzęk naczynioruchowy typu 2AAE 2 · AAE II · Nabyty obrzęk angioneurotyczny typu 2
csZískaný angioedém, typ 2AAE 2 · AAE II · Získaný angioneurotický edém, typ 2
ukНабутий ангіоневротичний набряк, тип 2AAE 2 · AAE II · Набутий ангіоневротичний набряк 2 типу
zh获得性血管性水肿2型获得性血管神经性水肿2型
trEdinsel anjiyoödem tip 2AAE 2 · AAE II · Edinsel anjiyonörotik ödem tip 2

Definition in:

2

Cross-references

qualifier = Orphanet mapping relation
SourceCodeQualifierICD relationValidation
ICD-10T78.3NTBTattributedvalidated
ICD-114A00.15NTBTindexvalidated
MONDO0015055Evalidated
UMLSC5680381Evalidated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

3

Classification

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

No children.

4

Genes

0 direct

Orphanet records no gene directly on this code.

5

Prevalence and incidence

0 records

No prevalence record in this release.

6

HPO phenotypes

Orphanet has no HPO annotation for this code in this release.

7

Sources for this card